Literature DB >> 2849648

Vasoactive intestinal polypeptide-secreting ganglioneuromatosis affecting the entire colon and rectum.

F J Rescorla1, D W Vane, J F Fitzgerald, K W West, J L Grosfeld.   

Abstract

This report describes a 7-year-old boy presenting with watery diarrhea, hypokalemia, and hypochlohydria associated with vasoactive intestinal polypeptide (VIP)-secreting ganglioneuromatosis involving the entire colon and rectum. The child's symptoms resolved following proctocolectomy, and the VIP levels returned to normal. Although 55 previous children have been reported with VIP-secreting tumors, this case is the first involving the entire colon and rectum.

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Year:  1988        PMID: 2849648     DOI: 10.1016/s0022-3468(88)80634-1

Source DB:  PubMed          Journal:  J Pediatr Surg        ISSN: 0022-3468            Impact factor:   2.545


  6 in total

1.  Ganglioneuromatous polyposis associated with juvenile polyps and a tubular adenoma.

Authors:  Shazia Rafiq; Hussein Hameer; Michael D Sitrin
Journal:  Dig Dis Sci       Date:  2005-03       Impact factor: 3.199

2.  A case of recurrent intestinal ganglioneuromatous polyposis accompanied with mesenteric schwannoma.

Authors:  Qi-Ming Wang; Dan Jiang; Hong-Ze Zeng; Yi Mou; Hang Yi; Wei Liu; Qi-Shan Zeng; Chun-Cheng Wu; Cheng-Wei Tang; Bing Hu
Journal:  Dig Dis Sci       Date:  2014-06-14       Impact factor: 3.199

Review 3.  Advances in understanding functional variations in the Hirschsprung disease spectrum (variant Hirschsprung disease).

Authors:  S W Moore
Journal:  Pediatr Surg Int       Date:  2016-12-17       Impact factor: 1.827

4.  A Case Series of Pediatric Intestinal Ganglioneuromatosis With Novel Phenotypic and Genotypic Profile.

Authors:  Yuan Fang; Ye Zhang; Rui Dong; Yi-Zhen Wang; Lian Chen; Gong Chen
Journal:  Front Med (Lausanne)       Date:  2022-06-16

Review 5.  Diffuse ganglioneuromatosis with plexiform neurofibromas limited to the gastrointestinal tract involving a large segment of small intestine.

Authors:  K Hirata; K Kitahara; Y Momosaka; H Kouho; N Nagata; H Hashimoto; H Itoh
Journal:  J Gastroenterol       Date:  1996-04       Impact factor: 7.527

Review 6.  Paraneoplastic manifestations in children.

Authors:  J H de Graaf; R Y Tamminga; W A Kamps
Journal:  Eur J Pediatr       Date:  1994-11       Impact factor: 3.183

  6 in total

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