Literature DB >> 28426870

A New Viscous Cysteamine Eye Drops Treatment for Ophthalmic Cystinosis: An Open-Label Randomized Comparative Phase III Pivotal Study.

Hong Liang1, Antoine Labbé2, Jeannie Le Mouhaër3, Céline Plisson3, Christophe Baudouin2.   

Abstract

Purpose: The purpose of this study was to evaluate the efficacy of new viscous cysteamine hydrochloride (CH) eye drops (vCH 0.55%) compared with standard CH 0.10% drops treatment.
Methods: This was an open-label, phase III, randomized, two-arm multicenter trial conducted at two centers in France. Cystinosis patients ≥2 years old were randomized 1:1 to receive eye drops, four times per day for 90 days in both eyes. We compared the superiority in reducing corneal cystine crystal density as assessed by in vivo confocal microscopy (IVCM). We also evaluated photophobia, corneal cystine crystal scores (CCCSs), and cystine crystal depth measured by optical coherence tomography. Safety objectives were to assess adverse events (AEs), local adverse drug reactions, and ocular safety parameters.
Results: We included 15 patients with vCH 0.55% and 16 patients with CH 0.10% drops for 90 days. The mean absolute change in IVCM total score at day 90 in the vCH 0.55% drops group (-4.6 ± 3.1) was significantly greater than and superior to the mean absolute change in the CH 0.10% drops group (-0.46 ± 3.38; P < 0.0001). Photophobia, CCCS, and corneal cystine crystal depth were significantly more improved in the vCH 0.55% drops group than in the CH 0.10% group. The most frequent local adverse drug reactions in both groups were stinging, burning, redness, and blurred vision. Conclusions: vCH 0.55% was effective in reducing corneal cystine crystal density and superior to treatment with CH 0.10% drops, which offer advantages over hospital pharmacy formulations and is a more preferable and convenient treatment option.

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Year:  2017        PMID: 28426870     DOI: 10.1167/iovs.16-21080

Source DB:  PubMed          Journal:  Invest Ophthalmol Vis Sci        ISSN: 0146-0404            Impact factor:   4.799


  17 in total

1.  Crystalline keratopathy in nephropathic cystinosis.

Authors:  Girish Chandra Bhatt; Amber Kumar; Brijesh Takkar
Journal:  Sudan J Paediatr       Date:  2019

2.  Effect of Storage Conditions on Stability of Ophthalmological Compounded Cysteamine Eye Drops.

Authors:  Ahmed Reda; Ann Van Schepdael; Erwin Adams; Prasanta Paul; David Devolder; Mohamed A Elmonem; Koenraad Veys; Ingele Casteels; Lambertus van den Heuvel; Elena Levtchenko
Journal:  JIMD Rep       Date:  2017-12-07

Review 3.  Adult complications of nephropathic cystinosis: a systematic review.

Authors:  Rachel Nora Kasimer; Craig B Langman
Journal:  Pediatr Nephrol       Date:  2020-02-03       Impact factor: 3.714

4.  A sustained release cysteamine microsphere/thermoresponsive gel eyedrop for corneal cystinosis improves drug stability.

Authors:  Jorge Jimenez; Michael A Washington; Jayde L Resnick; Ken K Nischal; Morgan V Fedorchak
Journal:  Drug Deliv Transl Res       Date:  2021-02-04       Impact factor: 4.617

Review 5.  Clinical Practice: A Proposed Standardized Ophthalmological Assessment for Patients with Cystinosis.

Authors:  Anne-Marie Pinxten; Minh-Tri Hua; Jennifer Simpson; Katharina Hohenfellner; Elena Levtchenko; Ingele Casteels
Journal:  Ophthalmol Ther       Date:  2017-05-05

6.  Nephropathic Cystinosis: Symptoms, Treatment, and Perspectives of a Systemic Disease.

Authors:  Sören Bäumner; Lutz T Weber
Journal:  Front Pediatr       Date:  2018-03-14       Impact factor: 3.418

7.  The Ocular Status of Cystinosis Patients Receiving a Hospital Pharmacy-Made Preparation of Cysteamine Eye Drops: A Case Series.

Authors:  Susmito Biswas; Krishanthy Sornalingam
Journal:  Ophthalmol Ther       Date:  2018-12-05

8.  Asymmetrical Ocular Manifestations of Nephropathic Cystinosis; A Case Report.

Authors:  Hala A Helmi; Jeylan El Mansoury; Selwa Al Hazzaa; Abdulaziz Al Zoba; Qais S Dirar
Journal:  Am J Case Rep       Date:  2019-09-04

Review 9.  Cysteamine hydrochloride eye drop solution for the treatment of corneal cystine crystal deposits in patients with cystinosis: an evidence-based review.

Authors:  Achini K Makuloluwa; Fatemeh Shams
Journal:  Clin Ophthalmol       Date:  2018-01-24

Review 10.  Latest Clinical Approaches in the Ocular Management of Cystinosis: A Review of Current Practice and Opinion from the Ophthalmology Cystinosis Forum.

Authors:  Susmito Biswas; Martha Gaviria; Luísa Malheiro; João Pedro Marques; Vincenzo Giordano; Hong Liang
Journal:  Ophthalmol Ther       Date:  2018-09-21
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