Literature DB >> 28334266

Phenopolis: an open platform for harmonization and analysis of genetic and phenotypic data.

Nikolas Pontikos1,2,3, Jing Yu4, Ismail Moghul5, Lucy Withington6, Fiona Blanco-Kelly2,3, Tom Vulliamy7, Tsz Lun Ernest Wong7, Cian Murphy1,8, Valentina Cipriani1,2,3, Alessia Fiorentino2, Gavin Arno2,3, Daniel Greene9,10, Julius O B Jacobsen11, Tristan Clark12, David S Gregory12, Andrea M Nemeth4, Stephanie Halford13, Chris F Inglehearn14, Susan Downes15, Graeme C Black16, Andrew R Webster2,3, Alison J Hardcastle2, Vincent Plagnol1.   

Abstract

SUMMARY: Phenopolis is an open-source web server providing an intuitive interface to genetic and phenotypic databases. It integrates analysis tools such as variant filtering and gene prioritization based on phenotype. The Phenopolis platform will accelerate clinical diagnosis, gene discovery and encourage wider adoption of the Human Phenotype Ontology in the study of rare genetic diseases.
AVAILABILITY AND IMPLEMENTATION: A demo of the website is available at https://phenopolis.github.io . If you wish to install a local copy, source code and installation instruction are available at https://github.com/phenopolis . The software is implemented using Python, MongoDB, HTML/Javascript and various bash shell scripts. CONTACT: n.pontikos@ucl.ac.uk. SUPPLEMENTARY INFORMATION: Supplementary data are available at Bioinformatics online.
© The Author (2017). Published by Oxford University Press. All rights reserved. For Permissions, please email: journals.permissions@oup.com

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Year:  2017        PMID: 28334266     DOI: 10.1093/bioinformatics/btx147

Source DB:  PubMed          Journal:  Bioinformatics        ISSN: 1367-4803            Impact factor:   6.937


  22 in total

1.  A novel missense mutation in HSF4 causes autosomal-dominant congenital lamellar cataract in a British family.

Authors:  V Berry; N Pontikos; A Moore; A C W Ionides; V Plagnol; M E Cheetham; M Michaelides
Journal:  Eye (Lond)       Date:  2017-12-15       Impact factor: 3.775

2.  Whole-genome sequencing reveals a recurrent missense mutation in the Connexin 46 (GJA3) gene causing autosomal-dominant lamellar cataract.

Authors:  Vanita Berry; Alexander C W Ionides; Nikolas Pontikos; Ismail Moghul; Anthony T Moore; Michael E Cheetham; Michel Michaelides
Journal:  Eye (Lond)       Date:  2018-05-01       Impact factor: 3.775

3.  Ectopic GRHL2 Expression Due to Non-coding Mutations Promotes Cell State Transition and Causes Posterior Polymorphous Corneal Dystrophy 4.

Authors:  Petra Liskova; Lubica Dudakova; Cerys J Evans; Karla E Rojas Lopez; Nikolas Pontikos; Dimitra Athanasiou; Hodan Jama; Josef Sach; Pavlina Skalicka; Viktor Stranecky; Stanislav Kmoch; Caroline Thaung; Martin Filipec; Michael E Cheetham; Alice E Davidson; Stephen J Tuft; Alison J Hardcastle
Journal:  Am J Hum Genet       Date:  2018-03-01       Impact factor: 11.025

4.  An Improved Phenotype-Driven Tool for Rare Mendelian Variant Prioritization: Benchmarking Exomiser on Real Patient Whole-Exome Data.

Authors:  Valentina Cipriani; Nikolas Pontikos; Gavin Arno; Panagiotis I Sergouniotis; Eva Lenassi; Penpitcha Thawong; Daniel Danis; Michel Michaelides; Andrew R Webster; Anthony T Moore; Peter N Robinson; Julius O B Jacobsen; Damian Smedley
Journal:  Genes (Basel)       Date:  2020-04-23       Impact factor: 4.096

5.  Novel homozygous splicing mutations in ARL2BP cause autosomal recessive retinitis pigmentosa.

Authors:  Alessia Fiorentino; Jing Yu; Gavin Arno; Nikolas Pontikos; Stephanie Halford; Suzanne Broadgate; Michel Michaelides; Keren J Carss; F Lucy Raymond; Michael E Cheetham; Andrew R Webster; Susan M Downes; Alison J Hardcastle
Journal:  Mol Vis       Date:  2018-08-31       Impact factor: 2.367

Review 6.  Systems Bioinformatics: increasing precision of computational diagnostics and therapeutics through network-based approaches.

Authors:  Anastasis Oulas; George Minadakis; Margarita Zachariou; Kleitos Sokratous; Marilena M Bourdakou; George M Spyrou
Journal:  Brief Bioinform       Date:  2019-05-21       Impact factor: 11.622

7.  Clinical and Genetic Characteristics of 18 Patients from 13 Japanese Families with CRX-associated retinal disorder: Identification of Genotype-phenotype Association.

Authors:  Yu Fujinami-Yokokawa; Kaoru Fujinami; Kazuki Kuniyoshi; Takaaki Hayashi; Shinji Ueno; Atsushi Mizota; Kei Shinoda; Gavin Arno; Nikolas Pontikos; Lizhu Yang; Xiao Liu; Hiroyuki Sakuramoto; Satoshi Katagiri; Kei Mizobuchi; Taro Kominami; Hiroko Terasaki; Natsuko Nakamura; Shuhei Kameya; Kazutoshi Yoshitake; Yozo Miyake; Toshihide Kurihara; Kazuo Tsubota; Hiroaki Miyata; Takeshi Iwata; Kazushige Tsunoda
Journal:  Sci Rep       Date:  2020-06-12       Impact factor: 4.379

8.  Rare coding variant analysis in a large cohort of Ashkenazi Jewish families with inflammatory bowel disease.

Authors:  E R Schiff; M Frampton; N Ben-Yosef; B E Avila; F Semplici; N Pontikos; S L Bloom; S A McCartney; R Vega; L B Lovat; E Wood; A Hart; E Israeli; D Crespi; M A Furman; S Mann; C D Murray; A W Segal; A P Levine
Journal:  Hum Genet       Date:  2018-08-22       Impact factor: 4.132

9.  Elevation in Cell Cycle and Protein Metabolism Gene Transcription in Inactive Colonic Tissue From Icelandic Patients With Ulcerative Colitis.

Authors:  Mathena Vinayaga-Pavan; Matthew Frampton; Nikolas Pontikos; Adam P Levine; Phillip J Smith; Jon G Jonasson; Einar S Björnsson; Anthony W Segal; Andrew M Smith
Journal:  Inflamm Bowel Dis       Date:  2019-01-10       Impact factor: 5.325

10.  The complex genetic landscape of familial MDS and AML reveals pathogenic germline variants.

Authors:  Ana Rio-Machin; Tom Vulliamy; Nele Hug; Amanda Walne; Kiran Tawana; Shirleny Cardoso; Alicia Ellison; Nikolas Pontikos; Jun Wang; Hemanth Tummala; Ahad Fahad H Al Seraihi; Jenna Alnajar; Findlay Bewicke-Copley; Hannah Armes; Michael Barnett; Adrian Bloor; Csaba Bödör; David Bowen; Pierre Fenaux; Andrew Green; Andrew Hallahan; Henrik Hjorth-Hansen; Upal Hossain; Sally Killick; Sarah Lawson; Mark Layton; Alison M Male; Judith Marsh; Priyanka Mehta; Rogier Mous; Josep F Nomdedéu; Carolyn Owen; Jiri Pavlu; Elspeth M Payne; Rachel E Protheroe; Claude Preudhomme; Nuria Pujol-Moix; Aline Renneville; Nigel Russell; Anand Saggar; Gabriela Sciuccati; David Taussig; Cynthia L Toze; Anne Uyttebroeck; Peter Vandenberghe; Brigitte Schlegelberger; Tim Ripperger; Doris Steinemann; John Wu; Joanne Mason; Paula Page; Susanna Akiki; Kim Reay; Jamie D Cavenagh; Vincent Plagnol; Javier F Caceres; Jude Fitzgibbon; Inderjeet Dokal
Journal:  Nat Commun       Date:  2020-02-25       Impact factor: 14.919

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