Literature DB >> 28329555

Dermatomyositis, clinically presenting with cutaneous ulcers, with histopathologic evidence of perforating collagenosis.

Rachel Rosenstein1, Kathryn Martires, Mitalee Christman, Vitaly Terushkin, Shane A Meehan, Nicole Seminara, Brian D Golden, Andrew G Franks.   

Abstract

Dermatomyositis is a systemic, autoimmune diseasewith a variety of clinical features that often includemyositis and characteristic cutaneous findings. Asubset of patients with dermatomyositis developcutaneous ulcers, often in the setting of vasculitis orvasculopathy. We present a case of dermatomyositiswith cutaneous ulcers that show perforatingcollagenosis on histopathologic examination.Acquired reactive perforating collagenosistypically occurs in the setting of diabetes mellitus,chronic renal failure, and other pruritic conditions,and this case represents a rare association withdermatomyositis, which may ultimately be helpful inelucidating the pathophysiology of this perforatingdisorder.

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Year:  2016        PMID: 28329555

Source DB:  PubMed          Journal:  Dermatol Online J        ISSN: 1087-2108


  1 in total

1.  Acquired Reactive Perforating Collagenosis - A Rare Cutaneous Manifestation of Anti-MDA5 Dermatomyositis.

Authors:  Teck Sheng Gan; Sook Yee Michelle Voo
Journal:  Indian J Dermatol       Date:  2022 Mar-Apr       Impact factor: 1.757

  1 in total

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