Jamie Golden1, Wesley E Barry1, Gene Jang1, Nam Nguyen1, David Bliss2. 1. Children's Hospital Los Angeles, Division of Pediatric Surgery, 4650 Sunset Blvd, Mailstop 100, Los Angeles, CA, 90027, USA. 2. Children's Hospital Los Angeles, Division of Pediatric Surgery, 4650 Sunset Blvd, Mailstop 100, Los Angeles, CA, 90027, USA. Dbliss@chla.usc.edu.
Abstract
INTRODUCTION: The Morgagni hernia (MH) accounts for 3-4% of congenital diaphragmatic hernias. There is a paucity of data regarding this rare defect. The purpose of this study is to describe the characteristics of children with MH, surgical approaches for repair, and patient outcomes. METHODS: Pediatric patients (ages 0-18) with a MH from 2002 to 2014 at a single, freestanding pediatric hospital were retrospectively reviewed. Patient presentation, demographics, operative methods and findings, and outcomes were evaluated. RESULTS: Twenty-six infants and children with a congenital MH were treated. There were 20 males (77%) and six females (23%) with a median age at diagnosis of 14.75 months (range 1 week to 13 years). Half were symptomatic. Sixteen hernias were repaired laparoscopically, nine by an open approach, and one laparoscopic converted to open. Colon was the most commonly herniated organ (N = 14). Hernia sacs were found in 22 patients of which, 20 were resected. Two patients underwent treatment with ECLS. There was one mortality in a patient who underwent repair on ECLS in the setting of an omphalocele and SVC obstruction. There were no recurrences in our sample. CONCLUSION: In this series, congenital MH appears to have a male predominance, frequently presents with pulmonary symptoms, and has excellent outcomes regardless of operative approach.
INTRODUCTION: The Morgagni hernia (MH) accounts for 3-4% of congenital diaphragmatic hernias. There is a paucity of data regarding this rare defect. The purpose of this study is to describe the characteristics of children with MH, surgical approaches for repair, and patient outcomes. METHODS: Pediatric patients (ages 0-18) with a MH from 2002 to 2014 at a single, freestanding pediatric hospital were retrospectively reviewed. Patient presentation, demographics, operative methods and findings, and outcomes were evaluated. RESULTS: Twenty-six infants and children with a congenital MH were treated. There were 20 males (77%) and six females (23%) with a median age at diagnosis of 14.75 months (range 1 week to 13 years). Half were symptomatic. Sixteen hernias were repaired laparoscopically, nine by an open approach, and one laparoscopic converted to open. Colon was the most commonly herniated organ (N = 14). Hernia sacs were found in 22 patients of which, 20 were resected. Two patients underwent treatment with ECLS. There was one mortality in a patient who underwent repair on ECLS in the setting of an omphalocele and SVC obstruction. There were no recurrences in our sample. CONCLUSION: In this series, congenital MH appears to have a male predominance, frequently presents with pulmonary symptoms, and has excellent outcomes regardless of operative approach.
Authors: Ahmed H Al-Salem; Mohammed Zamakhshary; Mohammed Al Mohaidly; Aayed Al-Qahtani; Mohamed Ramadan Abdulla; Mohamed Ibrahim Naga Journal: J Pediatr Surg Date: 2013-10-11 Impact factor: 2.545
Authors: R Lamas-Pinheiro; J Pereira; F Carvalho; P Horta; A Ochoa; M Knoblich; J Henriques; T Henriques-Coelho; J Correia-Pinto; P Casella; J Estevão-Costa Journal: Rev Port Pneumol (2006) Date: 2016-04-30