| Literature DB >> 28248720 |
Mario Fernando Ribeiro de Miranda, Josie Eiras Bisi Dos Santos, Silvia Ferreira Rodrigues Müller, Maraya de Jesus Semblano Bittencourt, Arival Cardoso de Brito, Jorge Nazareno da Silva Barros Junior, Ellen Maria Sampaio Xerfan.
Abstract
Hydroa vacciniforme (HV)-like lymphoma is a rare, usually fatal Epstein-Barr virus-driven lymphoproliferative disease affecting children from Asia, Mexico, and South America. Cutaneous manifestations imitate HV, a benign photodermatosis in which systemic symptoms are not observed, and spontaneous regression occurs later in adolescence or young adulthood. We report a case of HV-like lymphoma in a 12-year-old girl, descendent from an ancient Amazon indigenous tribe that, as far as we know, represents the second Brazilian case ever reported in the medical literature.Entities:
Mesh:
Year: 2018 PMID: 28248720 DOI: 10.1097/DAD.0000000000000846
Source DB: PubMed Journal: Am J Dermatopathol ISSN: 0193-1091 Impact factor: 1.533