Literature DB >> 28248720

Hydroa Vacciniforme-Like T-Cell Lymphoma: A Further Brazilian Case.

Mario Fernando Ribeiro de Miranda, Josie Eiras Bisi Dos Santos, Silvia Ferreira Rodrigues Müller, Maraya de Jesus Semblano Bittencourt, Arival Cardoso de Brito, Jorge Nazareno da Silva Barros Junior, Ellen Maria Sampaio Xerfan.   

Abstract

Hydroa vacciniforme (HV)-like lymphoma is a rare, usually fatal Epstein-Barr virus-driven lymphoproliferative disease affecting children from Asia, Mexico, and South America. Cutaneous manifestations imitate HV, a benign photodermatosis in which systemic symptoms are not observed, and spontaneous regression occurs later in adolescence or young adulthood. We report a case of HV-like lymphoma in a 12-year-old girl, descendent from an ancient Amazon indigenous tribe that, as far as we know, represents the second Brazilian case ever reported in the medical literature.

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Year:  2018        PMID: 28248720     DOI: 10.1097/DAD.0000000000000846

Source DB:  PubMed          Journal:  Am J Dermatopathol        ISSN: 0193-1091            Impact factor:   1.533


  1 in total

1.  Hydroa vacciniforme-like lymphoproliferative disorder in Ecuadorian children: A case series.

Authors:  Eduardo Garzón; John Jairo Dávila-Rodríguez
Journal:  Indian J Dermatol Venereol Leprol       Date:  2021-04-12       Impact factor: 2.545

  1 in total

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