Yara Dadalti Fragoso1, Tarso Adoni2, Joseph Bruno Bidin Brooks1, Sidney Gomes3, Marcus Vinicius Magno Goncalves4, Cassio Lemos Jovem5, Andre Palma da Cunha Matta6, Joao Filipe Oliveira7, Fabio Siquinelli7, Carlos Bernardo Tauil8, Guilherme Navarro Troiani1, Paulo Roberto Wille9. 1. Universidade Metropolitana de Santos, Departamento de Neurologia, Santos SP, Brasil. 2. Hospital Sirio-Libanes, Departamento de Neurologia, São Paulo SP, Brasil. 3. Hospital Beneficência Portuguesa e. 4. Centro Hospitalar Unimed, Departamento de Neurologia, Joinville SC, Brasil. 5. Hospital de Base do Distrito Federal, Departamento de Radiologia, Brasília DF, Brasil. 6. Universidade Federal Fluminense, Departamento de Neurologia, Niterói RJ, Brasil. 7. Universidade Regional de Blumenau, Departamento de Neurologia, Blumenau SC, Brasil. 8. Hospital de Base do Distrito Federal, Departamento de Neurologia, Brasília DF, Brasil. 9. IdHera, Departamento de Neurorradiologia, Joinville SC, Brasil.
Abstract
METHODS: Series of cases collected from Brazilian centers. RESULTS: We studied 13 cases of patients presenting with progressive histories of neurological dysfunction caused by SS-CNS. The most frequent clinical findings in these patients were progressive gait ataxia, hearing loss, hyperreflexia and cognitive dysfunction. The diagnoses of SS-CNS were made seven months to 30 years after the disease onset. CONCLUSION: SS-CNS is a rare disease that may remain undiagnosed for long periods. Awareness of this condition is essential for the clinician.
METHODS: Series of cases collected from Brazilian centers. RESULTS: We studied 13 cases of patients presenting with progressive histories of neurological dysfunction caused by SS-CNS. The most frequent clinical findings in these patients were progressive gait ataxia, hearing loss, hyperreflexia and cognitive dysfunction. The diagnoses of SS-CNS were made seven months to 30 years after the disease onset. CONCLUSION: SS-CNS is a rare disease that may remain undiagnosed for long periods. Awareness of this condition is essential for the clinician.