Lipoid Proteinosis.

A classical case of lipoid proteinosis in a 17 year old girl presenting with hoarseness of voice, thickened tongue, bullous lesions predominantly on pressure areas and varioliform scarring on the face and the extremities is reported. Her x-ray skull showed typical bean-shaped calcification in the limbic area. Histopathology revealed PAS stained amorphous deposits in the dermis and around the sweat glands.