Literature DB >> 28140668

A Family with Craniofrontonasal Syndrome: The First Report of Familial Cases of Craniofrontonasal Syndrome with Bilateral Cleft Lip and Palate.

Yoshikazu Inoue, Yoshiaki Sakamoto, Masanori Sugimoto, Hidehito Inagaki, Hiroko Boda, Masafumi Miyata, Hideteru Kato, Hiroki Kurahashi, Takayuki Okumoto.   

Abstract

Craniofrontonasal syndrome (CFNS) is a very rare genetic disorder, the common physical malformations of which include coronal synostosis, widely spaced eyes, clefting of the nasal tip, and various skeletal anomalies. Mutations of EFNB1, which encodes a member of the ephrin family of transmembrane ligands for Eph receptor tyrosine kinases, is the cause of CFNS. Although familial CFNS cases have been reported, no studies in the literature describe familial cases of CFNS expressing bilateral cleft lip and palate. Here, we describe a Japanese family with three cases of CFNS expressing bilateral cleft lip and palate.

Entities:  

Keywords:  EFNB1; bilateral cleft lip and palate; craniofrontonasal syndrome

Mesh:

Substances:

Year:  2018        PMID: 28140668     DOI: 10.1597/15-347

Source DB:  PubMed          Journal:  Cleft Palate Craniofac J        ISSN: 1055-6656


  2 in total

1.  Four novel mutations in EFNB1 in Indian patients with craniofrontonasal syndrome.

Authors:  Antonia Howaldt; Sheela Nampoothiri; Dhanya Yesodharan; Suhas Udayakumaran; Pramod Subash; Uwe Kornak
Journal:  J Hum Genet       Date:  2019-07-08       Impact factor: 3.172

2.  Aberrant cell segregation in the craniofacial primordium and the emergence of facial dysmorphology in craniofrontonasal syndrome.

Authors:  Terren K Niethamer; Teng Teng; Melanie Franco; Yu Xin Du; Christopher J Percival; Jeffrey O Bush
Journal:  PLoS Genet       Date:  2020-02-24       Impact factor: 5.917

  2 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.