| Literature DB >> 28124468 |
S L Gooskens1,2, M E Houwing1,2, G M Vujanic3, J S Dome4, T Diertens1, A Coulomb-l'Herminé5, J Godzinski6, K Pritchard-Jones7, N Graf8, M M van den Heuvel-Eibrink1.
Abstract
Congenital mesoblastic nephroma (CMN) is a rare pediatric renal tumor with low malignant potential that most commonly occurs early in infancy. Treatment strategies are based on the few published CMN series, while a significant number of CMN patients have been described in case reports. The aim of this narrative review was to create an up-to-date overview of the literature. Complete surgical removal is curative in most cases. The risk of treatment-related mortality (both surgery- and chemotherapy-related) is relatively high in the first weeks of life, indicating that these young patients deserve special attention with respect to timing and type of treatment.Entities:
Keywords: clinical characteristics; congenital mesoblastic nephroma; genetics; histology; infancy; outcome; renal tumor; review; treatment
Mesh:
Year: 2017 PMID: 28124468 DOI: 10.1002/pbc.26437
Source DB: PubMed Journal: Pediatr Blood Cancer ISSN: 1545-5009 Impact factor: 3.167