Hearing levels in the Cornelia de Lange syndrome. A report of seven cases.

Reports on the hearing levels of patients with the Cornelia de Lange syndrome in the literature are scarce. Pure-tone hearing thresholds and free field audiometry thresholds are presented for 7 patients with this syndrome. One of them showed a moderate sensorineural deafness and two others proved to have a slightly impaired hearing. Based on these results and on those from the literature it is concluded that hearing loss is an associated feature of the Cornelia de Lange syndrome.