Literature DB >> 27977405

Monitoring steroid replacement therapy in children with congenital adrenal hyperplasia.

Niels H Birkebaek, David M Hougaard, Arieh S Cohen.   

Abstract

BACKGROUND: The objective of this study was to compare the analysis of 17-hydroxyprogesterone (17-OHP) by radio-immunoassay (RIA) in serum with analysis by liquid chromatography tandem mass spectrometry (LC-MS/MS) on dried blood spot samples (DBSS) for monitoring therapy in children with congenital adrenal hyperplasia (CAH), and to investigate differences in 17-OHP values during the day.
METHODS: Fourteen children (8 females), median age 4.2 (0.3-16.0) years, were studied. Serum samples and DBSS were drawn before hydrocortisone dosing.
RESULTS: 17-OHP by LC-MS/MS in DBSS were highly correlated to 17-OHP by RIA in serum, r=0.956, p<0.01. A total of 26 three-time-point series were investigated. Using only the afternoon 17-OHP values to determine the hydrocortisone doses would have led to overdosing seven times and underdosing six times.
CONCLUSIONS: Good agreement was demonstrated between 17-OHP determination by RIA in serum and LC-MS/MS on DBSS. Multiple 17-OHP measurements per day are required to ensure sufficient hydrocortisone dose adjustment.

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Year:  2017        PMID: 27977405     DOI: 10.1515/jpem-2016-0203

Source DB:  PubMed          Journal:  J Pediatr Endocrinol Metab        ISSN: 0334-018X            Impact factor:   1.634


  2 in total

1.  Optimizing the Timing of Highest Hydrocortisone Dose in Children and Adolescents With 21-Hydroxylase Deficiency.

Authors:  Mariska A M Schröder; Antonius E van Herwaarden; Paul N Span; Erica L T van den Akker; Gianni Bocca; Sabine E Hannema; Hetty J van der Kamp; Sandra W K de Kort; Christiaan F Mooij; Dina A Schott; Saartje Straetemans; Vera van Tellingen; Janiëlle A van der Velden; Fred C G J Sweep; Hedi L Claahsen-van der Grinten
Journal:  J Clin Endocrinol Metab       Date:  2022-03-24       Impact factor: 5.958

2.  Diurnal salivary androstenedione and 17-hydroxyprogesterone levels in healthy volunteers for monitoring treatment efficacy of patients with congenital adrenal hyperplasia.

Authors:  Bas P H Adriaansen; Johannes S Kamphuis; Mariska A M Schröder; André J Olthaar; Carina Bock; André Brandt; Nike M M L Stikkelbroeck; Eef G W M Lentjes; Paul N Span; Fred C G J Sweep; Hedi L Claahsen-van der Grinten; Antonius E van Herwaarden
Journal:  Clin Endocrinol (Oxf)       Date:  2022-02-23       Impact factor: 3.523

  2 in total

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