Literature DB >> 27914924

The management of childhood liver diseases in adulthood.

Deepak Joshi1, Nitika Gupta2, Marianne Samyn3, Maesha Deheragoda3, Fabienne Dobbels4, Michael A Heneghan3.   

Abstract

An increasing number of patients with childhood liver disease survive into adulthood. These young adults are now entering adult services and require ongoing management. Aetiologies can be divided into liver diseases that develop in young adults which present to adult hepatologists i.e., biliary atresia and Alagille syndrome or liver diseases that occur in children/adolescents and adults i.e., autoimmune hepatitis or Wilson's disease. To successfully manage these young adults, a dynamic and responsive transition service is essential. In this review, we aim to describe the successful components of a transition service highlighting the importance of self-management support and a multi-disciplinary approach. We will also review some of the liver specific aetiologies which are unique to young adults, offering an update on pathogenesis, management and outcomes.
Copyright © 2016 European Association for the Study of the Liver. Published by Elsevier B.V. All rights reserved.

Entities:  

Keywords:  Adolescence; Autoimmune liver disease; Autoimmune sclerosing cholangitis; Biliary atresia; Cholestatic liver disease; Self-management; Transition

Mesh:

Year:  2016        PMID: 27914924     DOI: 10.1016/j.jhep.2016.11.013

Source DB:  PubMed          Journal:  J Hepatol        ISSN: 0168-8278            Impact factor:   25.083


  4 in total

Review 1.  TRANSITION of Pediatric Liver Transplant Patients to Adult Care: a Review.

Authors:  James P Stevens; Lori Hall; Nitika Arora Gupta
Journal:  Curr Gastroenterol Rep       Date:  2021-01-29

2.  Tacrolimus and Mycophenolate Mofetil as Second-Line Therapies for Pediatric Patients with Autoimmune Hepatitis.

Authors:  Cumali Efe; Haider Al Taii; Henriette Ytting; Niklas Aehling; Rahima A Bhanji; Hannes Hagström; Tugrul Purnak; Luigi Muratori; Mårten Werner; Paolo Muratori; Daniel Klintman; Thomas D Schiano; Aldo J Montano-Loza; Thomas Berg; Fin Stolze Larsen; Naim Alkhouri; Ersan Ozaslan; Michael A Heneghan; Eric M Yoshida; Staffan Wahlin
Journal:  Dig Dis Sci       Date:  2018-03-22       Impact factor: 3.199

3.  Nasobiliary drainage: an effective treatment for pruritus in cholestatic liver disease.

Authors:  Wafaa Ahmed; Rebecca Jeyaraj; David Reffitt; John Devlin; Abid Suddle; John Hunt; Michael A Heneghan; Phillip Harrison; Deepak Joshi
Journal:  Frontline Gastroenterol       Date:  2022-01-11

4.  Cholic acid for primary bile acid synthesis defects: a life-saving therapy allowing a favorable outcome in adulthood.

Authors:  Emmanuel Gonzales; Lorenza Matarazzo; Stéphanie Franchi-Abella; Alain Dabadie; Joseph Cohen; Dalila Habes; Sophie Hillaire; Catherine Guettier; Anne-Marie Taburet; Anne Myara; Emmanuel Jacquemin
Journal:  Orphanet J Rare Dis       Date:  2018-10-29       Impact factor: 4.123

  4 in total

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