Literature DB >> 27757165

A case of severe pyruvate kinase deficiency in a primigravida: successful outcome.

Sahar Mohamed1, Kenga Sivarajah1, Seema Chakravarti2.   

Abstract

Pyruvate kinase deficiency (PKD) is a rare non-spherocytic type of haemolytic anaemia. During pregnancy, women with severe PKD are at increased risk of infection, thrombosis, hypertension, fetal growth restriction and anaemia. Management of such cases requires close collaboration between a haematologist and an obstetrician. We report a case of severe PKD in pregnancy with good maternal and fetal outcome.

Entities:  

Keywords:  haematology; high-risk pregnancy; maternal-fetal medicine

Year:  2013        PMID: 27757165      PMCID: PMC5052770          DOI: 10.1258/OM.2012.120019

Source DB:  PubMed          Journal:  Obstet Med        ISSN: 1753-495X


  14 in total

1.  A specific erythrocyte glycolytic enzyme defect (pyruvate kinase) in three subjects with congenital non-spherocytic hemolytic anemia.

Authors:  W N VALENTINE; K R TANAKA; S MIWA
Journal:  Trans Assoc Am Physicians       Date:  1961

2.  Prenatal diagnosis of pyruvate kinase deficiency.

Authors:  L Baronciani; E Beutler
Journal:  Blood       Date:  1994-10-01       Impact factor: 22.113

3.  Pyruvate kinase deficiency hemolytic anemia: two successful pregnancy outcomes.

Authors:  J Fanning; R S Hinkle
Journal:  Am J Obstet Gynecol       Date:  1985-10-01       Impact factor: 8.661

Review 4.  Iron, infections, and anemia of inflammation.

Authors:  R L Jurado
Journal:  Clin Infect Dis       Date:  1997-10       Impact factor: 9.079

Review 5.  Pyruvate kinase deficiency complicating pregnancy.

Authors:  Joseph R Wax; Michael G Pinette; Angelina Cartin; Jacquelyn Blackstone
Journal:  Obstet Gynecol       Date:  2007-02       Impact factor: 7.661

6.  Hemolytic anemia and pyruvate kinase deficiency in pregnancy.

Authors:  K S Amankwah; B W Dick; S Dodge
Journal:  Obstet Gynecol       Date:  1980-03       Impact factor: 7.661

7.  Severe pyruvate kinase deficiency anemia. A case report.

Authors:  A Ghidini; V L Korker
Journal:  J Reprod Med       Date:  1998-08       Impact factor: 0.142

8.  Deferoxamine treatment during early pregnancy: absence of teratogenicity in two cases.

Authors:  E Vaskaridou; K Konstantopoulos; D Kyriakou; D Loukopoulos
Journal:  Haematologica       Date:  1993 May-Jun       Impact factor: 9.941

9.  Child abuse by intentional iron poisoning presenting as shock and persistent acidosis.

Authors:  Judy Black; Joseph A Zenel
Journal:  Pediatrics       Date:  2003-01       Impact factor: 7.124

Review 10.  Iron and thrombosis.

Authors:  Massimo Franchini; Giovanni Targher; Martina Montagnana; Giuseppe Lippi
Journal:  Ann Hematol       Date:  2007-12-08       Impact factor: 3.673

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