Literature DB >> 27692464

Long-Term Outcome of Classic and Incomplete PFAPA (Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Adenitis) Syndrome after Tonsillectomy.

Ulla Lantto1, Petri Koivunen2, Terhi Tapiainen3, Marjo Renko3.   

Abstract

OBJECTIVE: To compare the effectiveness of tonsillectomy and the long-term outcome of periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome in patients fulfilling the classic diagnostic criteria and in those with regularly recurring fever as the only symptom or with onset of symptoms after age 5 years or both. STUDY
DESIGN: We reviewed the medical records of 3852 children who underwent tonsillectomy between 1990 and 2007 and identified 108 children who did so because of regularly recurring fevers. The patients were invited to an outpatient visit and were classified into 2 groups: those who met (N = 58) and those who did not meet (N = 50) Thomas diagnostic criteria. We then compared the clinical profile and outcome of PFAPA symptoms after tonsillectomy between the 2 groups.
RESULTS: In the group that met Thomas criteria, 97% (56/58) had complete resolution of fever episodes after tonsillectomy; in the group that did not meet Thomas criteria (50/50) had complete resolution of fever episodes after tonsillectomy (P = .25). The clinical profile of the periodic fevers and the occurrence of other illnesses during follow-up were similar in both groups. Thomas criteria identified 56 of 106 patients responding to tonsillectomy.
CONCLUSIONS: Tonsillectomy was an effective treatment for patients with regularly recurring fever episodes who failed to meet the classic Thomas criteria. We suggest that PFAPA syndrome should be suspected and tonsillectomy considered in children with a late onset of symptoms (>5 years of age) or when fever is the only symptom during the episodes.
Copyright © 2016 Elsevier Inc. All rights reserved.

Entities:  

Keywords:  PFAPA; PFAPA syndrome; aphtas; criteria; definition; diagnostics; fever syndrome; recurrent fever; tonsillectomy

Mesh:

Year:  2016        PMID: 27692464     DOI: 10.1016/j.jpeds.2016.08.097

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  9 in total

1.  Risk factors for periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome: a case-control study.

Authors:  Sallamaaria Kettunen; Ulla Lantto; Petri Koivunen; Terhi Tapiainen; Matti Uhari; Marjo Renko
Journal:  Eur J Pediatr       Date:  2018-05-25       Impact factor: 3.183

2.  Children and Adults with PFAPA Syndrome: Similarities and Divergences in a Real-Life Clinical Setting.

Authors:  Ludovico Luca Sicignano; Donato Rigante; Beatrice Moccaldi; Maria Grazia Massaro; Stefano Delli Noci; Isabella Patisso; Giovanna Capozio; Elena Verrecchia; Raffaele Manna
Journal:  Adv Ther       Date:  2020-12-14       Impact factor: 3.845

3.  Unique histologic features of tonsils from patients with periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome.

Authors:  Kalpana Manthiram; Hernan Correa; Kelli Boyd; Joseph Roland; Kathryn Edwards
Journal:  Clin Rheumatol       Date:  2017-07-26       Impact factor: 2.980

4.  Periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis syndrome in children: a brief literature review.

Authors:  Cristina Terumy Okamoto; Hanne Lise Chaves; Mateus José Schmitz
Journal:  Rev Paul Pediatr       Date:  2022-06-10

5.  Undifferentiated recurrent fevers in pediatrics are clinically distinct from PFAPA syndrome but retain an IL-1 signature.

Authors:  Irene Luu; Javan Nation; Nathan Page; Daniela Carvalho; Anthony Magit; Wen Jiang; Shelby Leuin; Morgan Bliss; Marcella Bothwell; Matthew Brigger; Donald Kearns; Seth Pransky; Lori Broderick
Journal:  Clin Immunol       Date:  2021-02-24       Impact factor: 3.969

Review 6.  Periodic Fever in Children: Etiology and Diagnostic Challenges.

Authors:  Paola Carolina Espin Diaz; Kawaljeet Singh; Pawani Kher; Chaithanya Avanthika; Sharan Jhaveri; Yosra Saad; Shankhaneel Ghosh
Journal:  Cureus       Date:  2022-07-25

7.  Epidemiology and clinical features of PFAPA: a retrospective cohort study of 336 patients in western Sweden.

Authors:  Karin Rydenman; Hanna Fjeld; Josefine Hätting; Stefan Berg; Anders Fasth; Per Wekell
Journal:  Pediatr Rheumatol Online J       Date:  2022-09-15       Impact factor: 3.413

8.  Neither hereditary periodic fever nor periodic fever, aphthae, pharingitis, adenitis: Undifferentiated periodic fever in a tertiary pediatric center.

Authors:  Silvia De Pauli; Sara Lega; Serena Pastore; Domenico Leonardo Grasso; Anna Monica Rosaria Bianco; Giovanni Maria Severini; Alberto Tommasini; Andrea Taddio
Journal:  World J Clin Pediatr       Date:  2018-02-08

9.  The role of tonsillectomy in the Periodic Fever, Aphthous stomatitis, Pharyngitis and cervical Adenitis syndrome; a literature review.

Authors:  Jostein Førsvoll; Knut Øymar
Journal:  BMC Ear Nose Throat Disord       Date:  2018-02-22
  9 in total

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