Literature DB >> 27689944

Metabolic health profile in young adults with Prader-Willi syndrome: results of a 2-year randomized, placebo-controlled, crossover GH trial.

R J Kuppens1,2, N E Bakker1,2, E P C Siemensma1,2, S H Donze1,2, T Stijnen3, A C S Hokken-Koelega1,2.   

Abstract

CONTEXT: Patients with Prader-Willi syndrome (PWS) have an increased fat mass and decreased lean body mass. GH-treated young adults with PWS who have attained adult height benefit from continuation of growth hormone (GH) treatment, as GH maintained their improved body composition, whereas fat mass increased during the placebo period. Adults with PWS are predisposed to T2DM and cardiovascular disease. Whether GH affects metabolic health profile of this patient group is unknown.
OBJECTIVE: To investigate the effects of GH vs placebo on metabolic health, in young adults with PWS who were GH-treated for many years during childhood and had attained adult height (AH).
METHOD: A 2-year, randomized, double-blind, placebo-controlled crossover study with stratification for gender and BMI in 27 young adults with PWS. Intervention with GH (0·67 mg/m2 /day) and placebo, both for 1-year duration.
RESULTS: Compared to placebo, GH treatment resulted in similar glucose and insulin levels during oral glucose tolerance test. Only fasting glucose and insulin were slightly higher during GH vs placebo (+0·2 mmol/l and +18·4 pmol/l), although both remained within normal ranges in both phases. Blood pressure and lipid profile were similar after GH vs placebo. At baseline (AH) and during GH, no patients had metabolic syndrome, while 1 developed it during placebo treatment.
CONCLUSIONS: Growth hormone treatment has no adverse effects on metabolic health profile. Thus, GH-treated young adults with PWS who have attained AH benefit from continuation of GH treatment without safety concerns regarding metabolic health.
© 2016 The Authors. Clinical Endocrinology Published by John Wiley & Sons Ltd.

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Year:  2016        PMID: 27689944     DOI: 10.1111/cen.13247

Source DB:  PubMed          Journal:  Clin Endocrinol (Oxf)        ISSN: 0300-0664            Impact factor:   3.478


  5 in total

1.  Impact of transitional care on endocrine and anthropometric parameters in Prader-Willi syndrome.

Authors:  A C Paepegaey; M Coupaye; A Jaziri; F Ménesguen; B Dubern; M Polak; J M Oppert; M Tauber; G Pinto; C Poitou
Journal:  Endocr Connect       Date:  2018-04-17       Impact factor: 3.335

2.  A multidisciplinary approach to the clinical management of Prader-Willi syndrome.

Authors:  Jessica Duis; Pieter J van Wattum; Ann Scheimann; Parisa Salehi; Elly Brokamp; Laura Fairbrother; Anna Childers; Althea Robinson Shelton; Nathan C Bingham; Ashley H Shoemaker; Jennifer L Miller
Journal:  Mol Genet Genomic Med       Date:  2019-01-29       Impact factor: 2.183

3.  An Adapted Model for Transition to Adult Care in Young Adults with Prader-Willi Syndrome.

Authors:  Maria Pedersen; Charlotte Höybye
Journal:  J Clin Med       Date:  2021-05-06       Impact factor: 4.241

4.  Body composition, adipokines, bone mineral density and bone remodeling markers in relation to IGF-1 levels in adults with Prader-Willi syndrome.

Authors:  I Caroline van Nieuwpoort; Jos W R Twisk; Leopold M G Curfs; Paul Lips; Madeleine L Drent
Journal:  Int J Pediatr Endocrinol       Date:  2018-01-16

5.  Early start of growth hormone is associated with positive effects on auxology and metabolism in Prader-Willi-syndrome.

Authors:  Lucy Magill; Constanze Laemmer; Joachim Woelfle; Rolf Fimmers; Bettina Gohlke
Journal:  Orphanet J Rare Dis       Date:  2020-10-12       Impact factor: 4.123

  5 in total

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