Literature DB >> 27688878

How rare bone diseases have informed our knowledge of complex diseases.

Mark L Johnson1.   

Abstract

Rare bone diseases, generally defined as monogenic traits with either autosomal recessive or dominant patterns of inheritance, have provided a rich database of genes and associated pathways over the past 2-3 decades. The molecular genetic dissection of these bone diseases has yielded some major surprises in terms of the causal genes and/or involved pathways. The discovery of genes/pathways involved in diseases such as osteopetrosis, osteosclerosis, osteogenesis imperfecta and many other rare bone diseases have all accelerated our understanding of complex traits. Importantly these discoveries have provided either direct validation for a specific gene embedded in a group of genes within an interval identified through a complex trait genome-wide association study (GWAS) or based upon the pathway associated with a monogenic trait gene, provided a means to prioritize a large number of genes for functional validation studies. In some instances GWAS studies have yielded candidate genes that fall within linkage intervals associated with monogenic traits and resulted in the identification of causal mutations in those rare diseases. Driving all of this discovery is a complement of technologies such as genome sequencing, bioinformatics and advanced statistical analysis methods that have accelerated genetic dissection and greatly reduced the cost. Thus, rare bone disorders in partnership with GWAS have brought us to the brink of a new era of personalized genomic medicine in which the prevention and management of complex diseases will be driven by the molecular understanding of each individuals contributing genetic risks for disease.

Entities:  

Year:  2016        PMID: 27688878      PMCID: PMC5030722          DOI: 10.1038/bonekey.2016.69

Source DB:  PubMed          Journal:  Bonekey Rep        ISSN: 2047-6396


  98 in total

1.  Heterozygous mutations in ANKH, the human ortholog of the mouse progressive ankylosis gene, result in craniometaphyseal dysplasia.

Authors:  P Nürnberg; H Thiele; D Chandler; W Höhne; M L Cunningham; H Ritter; G Leschik; K Uhlmann; C Mischung; K Harrop; J Goldblatt; Z U Borochowitz; D Kotzot; F Westermann; S Mundlos; H S Braun; N Laing; S Tinschert
Journal:  Nat Genet       Date:  2001-05       Impact factor: 38.330

2.  LDL receptor-related protein 5 (LRP5) affects bone accrual and eye development.

Authors:  Y Gong; R B Slee; N Fukai; G Rawadi; S Roman-Roman; A M Reginato; H Wang; T Cundy; F H Glorieux; D Lev; M Zacharin; K Oexle; J Marcelino; W Suwairi; S Heeger; G Sabatakos; S Apte; W N Adkins; J Allgrove; M Arslan-Kirchner; J A Batch; P Beighton; G C Black; R G Boles; L M Boon; C Borrone; H G Brunner; G F Carle; B Dallapiccola; A De Paepe; B Floege; M L Halfhide; B Hall; R C Hennekam; T Hirose; A Jans; H Jüppner; C A Kim; K Keppler-Noreuil; A Kohlschuetter; D LaCombe; M Lambert; E Lemyre; T Letteboer; L Peltonen; R S Ramesar; M Romanengo; H Somer; E Steichen-Gersdorf; B Steinmann; B Sullivan; A Superti-Furga; W Swoboda; M J van den Boogaard; W Van Hul; M Vikkula; M Votruba; B Zabel; T Garcia; R Baron; B R Olsen; M L Warman
Journal:  Cell       Date:  2001-11-16       Impact factor: 41.582

3.  Targeted disruption of Cbfa1 results in a complete lack of bone formation owing to maturational arrest of osteoblasts.

Authors:  T Komori; H Yagi; S Nomura; A Yamaguchi; K Sasaki; K Deguchi; Y Shimizu; R T Bronson; Y H Gao; M Inada; M Sato; R Okamoto; Y Kitamura; S Yoshiki; T Kishimoto
Journal:  Cell       Date:  1997-05-30       Impact factor: 41.582

4.  Loss of the ClC-7 chloride channel leads to osteopetrosis in mice and man.

Authors:  U Kornak; D Kasper; M R Bösl; E Kaiser; M Schweizer; A Schulz; W Friedrich; G Delling; T J Jentsch
Journal:  Cell       Date:  2001-01-26       Impact factor: 41.582

5.  Disruption of Lrp4 function by genetic deletion or pharmacological blockade increases bone mass and serum sclerostin levels.

Authors:  Ming-Kang Chang; Ina Kramer; Thomas Huber; Bernd Kinzel; Sabine Guth-Gundel; Olivier Leupin; Michaela Kneissel
Journal:  Proc Natl Acad Sci U S A       Date:  2014-11-17       Impact factor: 11.205

6.  The Drosophila homolog of the mouse mammary oncogene int-1 is identical to the segment polarity gene wingless.

Authors:  F Rijsewijk; M Schuermann; E Wagenaar; P Parren; D Weigel; R Nusse
Journal:  Cell       Date:  1987-08-14       Impact factor: 41.582

7.  Taxonomy of rare genetic metabolic bone disorders.

Authors:  L Masi; D Agnusdei; J Bilezikian; D Chappard; R Chapurlat; L Cianferotti; J-P Devolgelaer; A El Maghraoui; S Ferrari; M K Javaid; J-M Kaufman; U A Liberman; G Lyritis; P Miller; N Napoli; E Roldan; S Papapoulos; N B Watts; M L Brandi
Journal:  Osteoporos Int       Date:  2015-06-13       Impact factor: 4.507

8.  Pycnodysostosis, a lysosomal disease caused by cathepsin K deficiency.

Authors:  B D Gelb; G P Shi; H A Chapman; R J Desnick
Journal:  Science       Date:  1996-08-30       Impact factor: 47.728

9.  Bone dysplasia sclerosteosis results from loss of the SOST gene product, a novel cystine knot-containing protein.

Authors:  M E Brunkow; J C Gardner; J Van Ness; B W Paeper; B R Kovacevich; S Proll; J E Skonier; L Zhao; P J Sabo; Y Fu; R S Alisch; L Gillett; T Colbert; P Tacconi; D Galas; H Hamersma; P Beighton; J Mulligan
Journal:  Am J Hum Genet       Date:  2001-02-09       Impact factor: 11.025

10.  Genetic determinants of trabecular and cortical volumetric bone mineral densities and bone microstructure.

Authors:  Lavinia Paternoster; Mattias Lorentzon; Terho Lehtimäki; Joel Eriksson; Mika Kähönen; Olli Raitakari; Marika Laaksonen; Harri Sievänen; Jorma Viikari; Leo-Pekka Lyytikäinen; Dan Mellström; Magnus Karlsson; Osten Ljunggren; Elin Grundberg; John P Kemp; Adrian Sayers; Maria Nethander; David M Evans; Liesbeth Vandenput; Jon H Tobias; Claes Ohlsson
Journal:  PLoS Genet       Date:  2013-02-21       Impact factor: 5.917

View more
  3 in total

1.  Identification of a Core Module for Bone Mineral Density through the Integration of a Co-expression Network and GWAS Data.

Authors:  Olivia L Sabik; Gina M Calabrese; Eric Taleghani; Cheryl L Ackert-Bicknell; Charles R Farber
Journal:  Cell Rep       Date:  2020-09-15       Impact factor: 9.423

Review 2.  Human Fibroblasts as a Model for the Study of Bone Disorders.

Authors:  Lauria Claeys; Nathalie Bravenboer; Elisabeth M W Eekhoff; Dimitra Micha
Journal:  Front Endocrinol (Lausanne)       Date:  2020-06-19       Impact factor: 5.555

3.  Development of the Bone Phenotype and microRNA Profile in Adults With Low-Density Lipoprotein Receptor-Related Protein 5-High Bone Mass (LRP5-HBM) Disease.

Authors:  Jens-Jacob Lindegaard Lauterlein; Fatma Gossiel; Moritz Weigl; Richard Eastell; Matthias Hackl; Pernille Hermann; Jens Bollerslev; Morten Frost
Journal:  JBMR Plus       Date:  2021-09-01
  3 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.