| Literature DB >> 27687732 |
Rubens Paulo A Salomão1, Maria Thereza Drumond Gama1, Flávio Moura Rezende Filho1, Fernanda Maggi1, José Luiz Pedroso2, Orlando G P Barsottini1.
Abstract
Herein, we report a patient that presented with late-onset progressive steppage gait, neuropathy and pes cavus, suggesting Charcot-Marie-Tooth (CMT) disease. Subsequent genetic investigation confirmed Friedreich's ataxia (FRDA). We demonstrate that late-onset Friedreich's ataxia (LOFA) may be a CMT mimicker. This case reinforces that other genetic conditions may clinically resemble CMT. The clinical similarities between CMT and FRDA include a symmetrical neuropathy (axonal in FRDA), steppage gait, and eventually scoliosis. We suggest that late-onset forms of hereditary neuropathies should be carefully evaluated, since LOFA may be a CMT mimicker.Entities:
Keywords: Charcot–Marie–Tooth disease; Friedreich’s ataxia; Hereditary ataxias; hereditary neuropathies
Mesh:
Year: 2017 PMID: 27687732 DOI: 10.1007/s12311-016-0822-9
Source DB: PubMed Journal: Cerebellum ISSN: 1473-4222 Impact factor: 3.847