Literature DB >> 27601065

Information and treatment decisions in severe spinal muscular atrophy: A parental follow-up.

Malin Lövgren1, Thomas Sejersen2, Ulrika Kreicbergs3.   

Abstract

INTRODUCTION: The parents of children with severe spinal muscular atrophy (SMA) face difficult ethical decisions regarding their child's treatment. This study explored the experience of parents of children with severe SMA concerning information and treatment decisions.
MATERIAL AND METHODS: This nationwide survey, conducted in 2013, is based on parents of children who were born in Sweden between 2000 and 2010 and later diagnosed with SMA type I or II where respiratory support was considered the first year of life (N = 61, participation rate: 87%). The survey involved parents' perception of the child's care and the questions used in this study covered information given and treatment decisions. Descriptive statistics were used.
RESULTS: None of the parents reported that the health care professionals made decisions concerning the child's treatment without informing them first, and 80% reported feeling confident about the decisions made. Of the bereaved parents, 11/48 (23%) reported that they got no information about respiratory support, compared to 2/13 (15%) of non-bereaved. Bereaved parents were more likely to report being satisfied with and understanding the information given about the illness and its treatment than non-bereaved parents.
CONCLUSION: All parents reported having been informed before treatment decisions were made and a vast majority reported feeling confident about the decisions. However, a quarter of the parents declined to have received information about respiratory support, which indicates that the parents did not sufficiently understand the available respiratory treatment options, and that their children may not receive the kind of care that is recommended in guidelines.
Copyright © 2016 European Paediatric Neurology Society. Published by Elsevier Ltd. All rights reserved.

Entities:  

Keywords:  Information; Parental perception; Spinal muscular atrophy; Treatment decision

Mesh:

Year:  2016        PMID: 27601065     DOI: 10.1016/j.ejpn.2016.08.008

Source DB:  PubMed          Journal:  Eur J Paediatr Neurol        ISSN: 1090-3798            Impact factor:   3.140


  2 in total

1.  "Suddenly we have hope that there is a future": two families' narratives when a child with spinal muscular atrophy receives a new drug.

Authors:  Elin Hjorth; Malin Lövgren; Ulrika Kreicbergs; Thomas Sejersen; Eric Asaba
Journal:  Int J Qual Stud Health Well-being       Date:  2021-12

2.  Experiences of caregivers of children with spinal muscular atrophy participating in the expanded access program for nusinersen: a longitudinal qualitative study.

Authors:  Petra Kiefer; Janbernd Kirschner; Astrid Pechmann; Thorsten Langer
Journal:  Orphanet J Rare Dis       Date:  2020-07-29       Impact factor: 4.123

  2 in total

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