| Literature DB >> 27582999 |
Alun Yewlett1, Jeff Kitson1, Andrew Redfern2, Chris Smith1.
Abstract
Fibrodysplasia progressiva ossificans (FPO) is an extremely rare condition characterized by abnormal heterotopic bone formation. The condition is eponymously known as 'stoneman' disease because patients can become effectively entombed within abnormal heterotopic bone. We present the first known case of a diaphyseal humeral fracture managed conservatively in an adult patient with this condition. This patient already had a pre-existing bony bar from a fusion mass involving the thoracic spine, scapula and ribs to her proximal humerus splinting the arm in a position of adduction with the palm of her hand facing towards her groin. This patient also suffered a concomitant unstable cervical spinal fracture for which full spinal precautions were needed. As a result of the rapid bone forming nature of her condition, the humeral fracture was placed in a position where the hand would face outwards to make perineal care and personal hygiene easier in that the fracture was expected to unite in this new position as a result of her FPO.Entities:
Keywords: case report; conservative treatment; fibrodysplasia progressiva ossificans; humeral fracture
Year: 2015 PMID: 27582999 PMCID: PMC4935172 DOI: 10.1177/1758573215598498
Source DB: PubMed Journal: Shoulder Elbow ISSN: 1758-5732