Literature DB >> 27555301

Prevalence of elevated liver enzymes in children with cystic fibrosis diagnosed by newborn screen.

Samantha A Woodruff1, Marci K Sontag2, Frank J Accurso3, Ronald J Sokol1, Michael R Narkewicz4.   

Abstract

BACKGROUND: Prevalence and risks for elevated liver enzymes have not been studied systematically in children with CF identified by newborn screen.
METHODS: 298 CF children identified by newborn screen since 1982. AST, ALT and GGT tested at annual visits. Percent of children with 1 or ≥2 values of elevated AST, ALT and GGT determined. Relationship of liver enzymes to clinical factors or subsequent liver disease was analyzed
RESULTS: At least one abnormal value for AST (63%), ALT (93%) and ALT ≥1.5× ULN (52%) occurred by 21years of age. Liver enzyme elevations were not correlated with CFTR mutation, meconium ileus or ethnicity. AST and GGT ≥1.5× ULN were associated with later advanced liver disease HR (CI) 6.53 (2.02-21.1) and 4.03 (1.15-13.45), respectively.
CONCLUSIONS: Elevated liver enzymes are common during childhood in CF patients identified by newborn screen. Elevated AST and GGT may be markers for risk of advanced liver disease.
Copyright © 2016 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.

Entities:  

Keywords:  Cystic fibrosis liver disease; Newborn screening

Mesh:

Substances:

Year:  2016        PMID: 27555301     DOI: 10.1016/j.jcf.2016.08.002

Source DB:  PubMed          Journal:  J Cyst Fibros        ISSN: 1569-1993            Impact factor:   5.482


  7 in total

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Authors:  Keyan Zarei; David K Meyerholz; David A Stoltz
Journal:  Physiol Rep       Date:  2021-07

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  7 in total

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