Literature DB >> 27504332

Benign Recurrent Intrahepatic Cholestasis in a Young Adult.

Prabhat Kumar1, Riyaz Charaniya2, Arvind Ahuja3, Sakshi Mittal1, Ratnakar Sahoo4.   

Abstract

Benign Recurrent Intrahepatic Cholestasis (BRIC) is a rare genetic disorder characterized by recurrent episodes of cholestatic jaundice. The initial episode of jaundice generally occurs before second decade of life and can persist for several weeks to months before resolving spontaneously. It is a benign disease and even after repeated episodes of jaundice, fibrosis of liver cell does not occur. We had a young adult patient who was having recurrent episodes of cholestatic jaundice with intervening symptom free period for last 20 years. He had first episode of jaundice at the age of eight and since then had several similar episodes. Diagnosis was made by classical clinical presentation and histopathological findings. We intend to report this case due to rarity of this disease in India.

Entities:  

Keywords:  Cholestatic jaundice; Pruritus; Rifampicin

Year:  2016        PMID: 27504332      PMCID: PMC4963692          DOI: 10.7860/JCDR/2016/18917.7924

Source DB:  PubMed          Journal:  J Clin Diagn Res        ISSN: 0973-709X


  11 in total

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Authors:  Esteban Mezey; Clinton Burns; James F Burdick; Hayden G Braine
Journal:  Am J Gastroenterol       Date:  2002-02       Impact factor: 10.864

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Journal:  Arq Gastroenterol       Date:  2001-12-05

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Journal:  Gastroenterology       Date:  1967-03       Impact factor: 22.682

6.  Ileal exclusion for Byler's disease: an alternative surgical approach with promising early results for pruritus.

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Journal:  J Pediatr Surg       Date:  1998-02       Impact factor: 2.545

Review 7.  Familial cholestasis: progressive familial intrahepatic cholestasis, benign recurrent intrahepatic cholestasis and intrahepatic cholestasis of pregnancy.

Authors:  Wendy L van der Woerd; Saskia W C van Mil; Janneke M Stapelbroek; Leo W J Klomp; Stan F J van de Graaf; Roderick H J Houwen
Journal:  Best Pract Res Clin Gastroenterol       Date:  2010-10       Impact factor: 3.043

8.  The molecular adsorbents recycling system as a liver support system based on albumin dialysis: a summary of preclinical investigations, prospective, randomized, controlled clinical trial, and clinical experience from 19 centers.

Authors:  Jan Stange; Tarek I Hassanein; Ravindra Mehta; Steffen R Mitzner; Robert H Bartlett
Journal:  Artif Organs       Date:  2002-02       Impact factor: 3.094

Review 9.  Benign recurrent intrahepatic cholestasis.

Authors:  Velimir A Luketic; Mitchell L Shiffman
Journal:  Clin Liver Dis       Date:  2004-02       Impact factor: 6.126

10.  Benign recurrent intrahepatic cholestasis type 2 is caused by mutations in ABCB11.

Authors:  Saskia W C van Mil; Wendy L van der Woerd; Gerda van der Brugge; Ekkehard Sturm; Peter L M Jansen; Laura N Bull; Inge E T van den Berg; Ruud Berger; Roderick H J Houwen; Leo W J Klomp
Journal:  Gastroenterology       Date:  2004-08       Impact factor: 22.682

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