Literature DB >> 27483107

Oral Lesions in Pycnodysostosis Syndrome: Eleven Years of Follow-Up.

Viviane Palmeira da Silva1, Fernanda Visioli, Bruna Jalfim Maraschin, Juliana Andrade Cardoso, Gleicy Gabriela V S C Falcão, Márcio Campos de Oliveira, Jener Gonçalves de Farias.   

Abstract

Pycnodysostosis is a rare genetic disease that is characterized by osteosclerosis, short stature, and bone fragility. There are not cases of gnathic bones lesions reported on the international literature. This study aims to describe a clinical case of a 10-year-old girl with pycnodysostosis syndrome and an uncommon association with 4 distinct lesions (dentigerous cyst, central giant cell lesions, and 2 fibro-osseous lesions).

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Year:  2016        PMID: 27483107     DOI: 10.1097/SCS.0000000000002952

Source DB:  PubMed          Journal:  J Craniofac Surg        ISSN: 1049-2275            Impact factor:   1.046


  1 in total

Review 1.  Osteomyelitis of the jaws in patients with pycnodysostosis: a systematic review.

Authors:  Glória Maria de França; Fernanda Aragão Felix; Everton Freitas de Morais; Maurília Raquel de Souto Medeiros; Ana Cláudia de Macedo Andrade; Hébel Cavalcanti Galvão
Journal:  Braz J Otorhinolaryngol       Date:  2021-01-29
  1 in total

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