| Literature DB >> 27483107 |
Viviane Palmeira da Silva1, Fernanda Visioli, Bruna Jalfim Maraschin, Juliana Andrade Cardoso, Gleicy Gabriela V S C Falcão, Márcio Campos de Oliveira, Jener Gonçalves de Farias.
Abstract
Pycnodysostosis is a rare genetic disease that is characterized by osteosclerosis, short stature, and bone fragility. There are not cases of gnathic bones lesions reported on the international literature. This study aims to describe a clinical case of a 10-year-old girl with pycnodysostosis syndrome and an uncommon association with 4 distinct lesions (dentigerous cyst, central giant cell lesions, and 2 fibro-osseous lesions).Entities:
Mesh:
Year: 2016 PMID: 27483107 DOI: 10.1097/SCS.0000000000002952
Source DB: PubMed Journal: J Craniofac Surg ISSN: 1049-2275 Impact factor: 1.046