Literature DB >> 27437288

Subcutaneous Panniculitis-Like T-Cell Lymphoma: A Rare Tumour.

Mohan Varadanayakanahalli Bhojaraja1, Pradeep Kumar Reddy Kistampally2, Karthik S Udupa3, Joseph Thomas4.   

Abstract

Subcutaneous Panniculitis like T cell Lymphoma (SPTCL) is an uncommon variant and poorly differentiated type of cutaneous T cell lymphoma. Here we describe the case of a 19-year-old female who presented with swelling of left half of the face with no regional lymphadenopathy and hepatosplenomegaly which was initially misdiagnosed as a benign cutaneous condition by various practitioners. Histopathological examination revealed diffuse infiltration of subcutaneous plane by small to medium sized atypical lymphocytes. Immunohistochemistry showed CD3, CD8 and βF-1 positivity; CD20, CD56, Epstein Barr Virus (EBV) and TCR-δ negativity. Clinical profile, histopathology and immunohistochemical analysis yielded a diagnosis of SPTCL. Thus cases with atypical and nonresolving dermatological lesions should raise a suspicion of SPTCL as diagnosis against other benign conditions.

Entities:  

Keywords:  Atypical lymphocytes; Cutaneous condition; Face; Non resolving

Year:  2016        PMID: 27437288      PMCID: PMC4948464          DOI: 10.7860/JCDR/2016/18458.7824

Source DB:  PubMed          Journal:  J Clin Diagn Res        ISSN: 0973-709X


  12 in total

1.  Fatal subcutaneous panniculitis-like T-cell lymphoma with interface change and dermal mucin, a dead ringer for lupus erythematosus.

Authors:  Linglei Ma; Bizhan Bandarchi; Earl J Glusac
Journal:  J Cutan Pathol       Date:  2005-05       Impact factor: 1.587

2.  Subcutaneous panniculitic T-cell lymphoma is a tumor of cytotoxic T lymphocytes.

Authors:  S Kumar; L Krenacs; J Medeiros; K S Elenitoba-Johnson; T C Greiner; L Sorbara; D W Kingma; M Raffeld; E S Jaffe
Journal:  Hum Pathol       Date:  1998-04       Impact factor: 3.466

3.  Local facial edema: a novel presentation of subcutaneous panniculitis-like T-cell lymphoma in a 30-year-old Iranian woman.

Authors:  Farid Kosari; Sanam Akbarzadeh Hosseini
Journal:  Acta Med Iran       Date:  2014

Review 4.  The new World Health Organization-European Organization for Research and Treatment of Cancer classification for cutaneous lymphomas: a practical marriage of two giants.

Authors:  D N Slater
Journal:  Br J Dermatol       Date:  2005-11       Impact factor: 9.302

Review 5.  WHO-EORTC classification for cutaneous lymphomas.

Authors:  Rein Willemze; Elaine S Jaffe; Günter Burg; Lorenzo Cerroni; Emilio Berti; Steven H Swerdlow; Elisabeth Ralfkiaer; Sergio Chimenti; José L Diaz-Perez; Lyn M Duncan; Florent Grange; Nancy Lee Harris; Werner Kempf; Helmut Kerl; Michael Kurrer; Robert Knobler; Nicola Pimpinelli; Christian Sander; Marco Santucci; Wolfram Sterry; Maarten H Vermeer; Janine Wechsler; Sean Whittaker; Chris J L M Meijer
Journal:  Blood       Date:  2005-02-03       Impact factor: 22.113

6.  Positron emission tomography in subcutaneous panniculitis-like T-cell lymphoma.

Authors:  Victor R Rodriguez; Aparna Joshi; Fangyu Peng; Raja M Rabah; Paul T Stockmann; Süreyya Savaşan
Journal:  Pediatr Blood Cancer       Date:  2009-03       Impact factor: 3.167

7.  T-cell lymphoma involving subcutaneous tissue. A clinicopathologic entity commonly associated with hemophagocytic syndrome.

Authors:  C L Gonzalez; L J Medeiros; R M Braziel; E S Jaffe
Journal:  Am J Surg Pathol       Date:  1991-01       Impact factor: 6.394

Review 8.  Immunophenotypic and molecular features, clinical outcomes, treatments, and prognostic factors associated with subcutaneous panniculitis-like T-cell lymphoma: a systematic analysis of 156 patients reported in the literature.

Authors:  Ronald S Go; Susan M Wester
Journal:  Cancer       Date:  2004-09-15       Impact factor: 6.860

9.  An ultrastructural study of cutaneous panniculitis-like T-cell lymphoma: cytoplasmic granules and active cellular and cell-to-matrix interaction mimic cytotoxic T-cells.

Authors:  Kazuto Yamazaki
Journal:  Ultrastruct Pathol       Date:  2002 May-Jun       Impact factor: 1.094

10.  Subcutaneous panniculitis-like T-cell lymphoma: definition, classification, and prognostic factors: an EORTC Cutaneous Lymphoma Group Study of 83 cases.

Authors:  Rein Willemze; Patty M Jansen; Lorenzo Cerroni; Emilio Berti; Marco Santucci; Chalid Assaf; Marijke R Canninga-van Dijk; Agnes Carlotti; Marie-Louise Geerts; Sonja Hahtola; Michael Hummel; Leila Jeskanen; Werner Kempf; Cesare Massone; Pablo L Ortiz-Romero; Marco Paulli; Tony Petrella; Annamari Ranki; José L Rodriguez Peralto; Alistair Robson; Nancy J Senff; Maarten H Vermeer; Janine Wechsler; Sean Whittaker; Chris J L M Meijer
Journal:  Blood       Date:  2007-10-12       Impact factor: 22.113

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