Literature DB >> 27351440

Migalastat: First Global Approval.

Anthony Markham1.   

Abstract

Migalastat (Galafold™)-a small molecule drug developed by Amicus Therapeutics that restores the activity of specific mutant forms of α-galactosidase-has been approved for the treatment of Fabry disease in the EU in patients with amenable mutations. Fabry disease is a rare disorder that results in a deficiency or absence of α-galactosidase, leading to accumulation of globotriaosylceramide in the lysosomes of various cells. This article summarizes the milestones in the development of migalastat leading to this first approval in the EU for the long-term treatment of adults and adolescents aged ≥16 years with a confirmed diagnosis of Fabry disease.

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Year:  2016        PMID: 27351440     DOI: 10.1007/s40265-016-0607-y

Source DB:  PubMed          Journal:  Drugs        ISSN: 0012-6667            Impact factor:   9.546


  5 in total

1.  A Phase 2 study of migalastat hydrochloride in females with Fabry disease: selection of population, safety and pharmacodynamic effects.

Authors:  R Giugliani; S Waldek; D P Germain; K Nicholls; D G Bichet; J K Simosky; A C Bragat; J P Castelli; E R Benjamin; P F Boudes
Journal:  Mol Genet Metab       Date:  2013-01-26       Impact factor: 4.797

2.  Relative bioavailability and the effect of meal type and timing on the pharmacokinetics of migalastat in healthy volunteers.

Authors:  Franklin K Johnson; Paul N Mudd; Salim G Janmohamed
Journal:  Clin Pharmacol Drug Dev       Date:  2014-12-02

3.  Co-administration with the pharmacological chaperone AT1001 increases recombinant human α-galactosidase A tissue uptake and improves substrate reduction in Fabry mice.

Authors:  Elfrida R Benjamin; Richie Khanna; Adriane Schilling; John J Flanagan; Lee J Pellegrino; Nastry Brignol; Yi Lun; Darlene Guillen; Brian E Ranes; Michelle Frascella; Rebecca Soska; Jessie Feng; Leo Dungan; Brandy Young; David J Lockhart; Kenneth J Valenzano
Journal:  Mol Ther       Date:  2012-01-03       Impact factor: 11.454

4.  Safety and pharmacodynamic effects of a pharmacological chaperone on α-galactosidase A activity and globotriaosylceramide clearance in Fabry disease: report from two phase 2 clinical studies.

Authors:  Dominique P Germain; Roberto Giugliani; Derralynn A Hughes; Atul Mehta; Kathy Nicholls; Laura Barisoni; Charles J Jennette; Alexander Bragat; Jeff Castelli; Sheela Sitaraman; David J Lockhart; Pol F Boudes
Journal:  Orphanet J Rare Dis       Date:  2012-11-24       Impact factor: 4.123

5.  Oral Migalastat HCl Leads to Greater Systemic Exposure and Tissue Levels of Active α-Galactosidase A in Fabry Patients when Co-Administered with Infused Agalsidase.

Authors:  David G Warnock; Daniel G Bichet; Myrl Holida; Ozlem Goker-Alpan; Kathy Nicholls; Mark Thomas; Francois Eyskens; Suma Shankar; Mathews Adera; Sheela Sitaraman; Richie Khanna; John J Flanagan; Brandon A Wustman; Jay Barth; Carrolee Barlow; Kenneth J Valenzano; David J Lockhart; Pol Boudes; Franklin K Johnson
Journal:  PLoS One       Date:  2015-08-07       Impact factor: 3.240

  5 in total
  22 in total

Review 1.  Emptying the stores: lysosomal diseases and therapeutic strategies.

Authors:  Frances M Platt
Journal:  Nat Rev Drug Discov       Date:  2017-11-17       Impact factor: 84.694

2.  Fabry disease: A pharmacological chaperone on the horizon.

Authors:  Martina Gaggl; Gere Sunder-Plassmann
Journal:  Nat Rev Nephrol       Date:  2016-09-26       Impact factor: 28.314

3.  Drug Repositioning for Fabry Disease: Acetylsalicylic Acid Potentiates the Stabilization of Lysosomal Alpha-Galactosidase by Pharmacological Chaperones.

Authors:  Maria Monticelli; Ludovica Liguori; Mariateresa Allocca; Andrea Bosso; Giuseppina Andreotti; Jan Lukas; Maria Chiara Monti; Elva Morretta; Maria Vittoria Cubellis; Bruno Hay Mele
Journal:  Int J Mol Sci       Date:  2022-05-04       Impact factor: 6.208

Review 4.  Lysosomal storage diseases.

Authors:  Frances M Platt; Alessandra d'Azzo; Beverly L Davidson; Elizabeth F Neufeld; Cynthia J Tifft
Journal:  Nat Rev Dis Primers       Date:  2018-10-01       Impact factor: 52.329

5.  Screening of Fabry disease in patients with end-stage renal disease of unknown etiology: the first Thailand study.

Authors:  Objoon Trachoo; Paisan Jittorntam; Sarunpong Pibalyart; Saowanee Kajanachumphol; Norasak Suvachittanont; Suthep Patputthipong; Piyatida Chuengsaman; Arkom Nongnuch
Journal:  J Biomed Res       Date:  2016-10-17

6.  Migalastat improves diarrhea in patients with Fabry disease: clinical-biomarker correlations from the phase 3 FACETS trial.

Authors:  Raphael Schiffmann; Daniel G Bichet; Ana Jovanovic; Derralynn A Hughes; Roberto Giugliani; Ulla Feldt-Rasmussen; Suma P Shankar; Laura Barisoni; Robert B Colvin; J Charles Jennette; Fred Holdbrook; Andrew Mulberg; Jeffrey P Castelli; Nina Skuban; Jay A Barth; Kathleen Nicholls
Journal:  Orphanet J Rare Dis       Date:  2018-04-27       Impact factor: 4.123

7.  E-Learning for Rare Diseases: An Example Using Fabry Disease.

Authors:  Chiara Cimmaruta; Ludovica Liguori; Maria Monticelli; Giuseppina Andreotti; Valentina Citro
Journal:  Int J Mol Sci       Date:  2017-09-24       Impact factor: 5.923

8.  Probing the Inhibitor versus Chaperone Properties of sp²-Iminosugars towards Human β-Glucocerebrosidase: A Picomolar Chaperone for Gaucher Disease.

Authors:  Teresa Mena-Barragán; M Isabel García-Moreno; Alen Sevšek; Tetsuya Okazaki; Eiji Nanba; Katsumi Higaki; Nathaniel I Martin; Roland J Pieters; José M García Fernández; Carmen Ortiz Mellet
Journal:  Molecules       Date:  2018-04-17       Impact factor: 4.411

9.  Enzyme replacement therapy and white matter hyperintensity progression in Fabry disease.

Authors:  James D Stefaniak; Laura M Parkes; Adrian R Parry-Jones; Gillian M Potter; Andy Vail; Ana Jovanovic; Craig J Smith
Journal:  Neurology       Date:  2018-09-12       Impact factor: 9.910

10.  Inhibition of Mitochondrial Complex I Impairs Release of α-Galactosidase by Jurkat Cells.

Authors:  Jonathan R A Lambert; Steven J Howe; Ahad A Rahim; Derek G Burke; Simon J R Heales
Journal:  Int J Mol Sci       Date:  2019-09-05       Impact factor: 5.923

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