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Literature DB >> 27195197

A case of split notochord syndrome: Presenting with respiratory failure in the neonatal period.

Yesim Coskun¹, Ipek Akman¹, Mustafa Kemal Demir², Ozlem Yapicier³, Salih Somuncu⁴.

Abstract

Split notochord syndrome (SNS) is a very rare congenital anomaly. This report describes a male newborn with a neuroenteric cyst in the posterior mediastinum and multiple vertebrae anomalies presenting with respiratory failure and pulmonary hypertension. This report also discusses the embryological development and the etiologic theories of SNS.

Entities: Disease

Keywords: Split notochord syndrome; newborn; respiratory failure

Year: 2016 PMID： 27195197 PMCID： PMC4869579 DOI： 10.5582/irdr.2016.01010

Source DB: PubMed Journal: Intractable Rare Dis Res ISSN： 2186-3644

11 in total

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Journal: J Pediatr Surg Date: 1975-08 Impact factor: 2.545

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Authors: Gabrielle H van Ramshorst; Maarten H Lequin; Grazia M S Mancini; Cornelis P van de Ven
Journal: J Pediatr Surg Date: 2006-12 Impact factor: 2.545

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Journal: J Pediatr Surg Date: 2007-05 Impact factor: 2.545

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Authors: Dakshesh Parikh; Madan Samuel
Journal: Pediatr Pulmonol Date: 2005-12

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Authors: N Razack; L K Page
Journal: Neurosurgery Date: 1995-11 Impact factor: 4.654

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Authors: M H Kheradpir; M R Ameri
Journal: Z Kinderchir Date: 1983-06

A case of split notochord syndrome: Presenting with respiratory failure in the neonatal period.

1. The split notochord syndrome.

2. A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis.

3. Neurenteric cyst--a case report of this rare disorder.

4. Congenital cystic lung lesions: is surgical resection essential?

5. Split notochord syndrome: case report.

6. Dorsal herniation of the gut with posterior opening of the terminal colon: a rare manifestation of the split notochord syndrome.

Review 7. Split notochord syndrome variant: prenatal findings and neonatal management.

8. Split notochord syndrome associated with dorsal neuroenteric fistula: A rare entity.

9. Split notochord syndrome with neuroenteric fistula.

10. Recurrent hemoptysis and a mass in the thorax in an infant: the split notochord syndrome.

1. Prenatal diagnosis of Fetal notochord syndrome: A case report and review of the literature.

2. A Case of Split Notochord Syndrome with Left Congenital Diaphragmatic Hernia: A Rare Association.