Literature DB >> 27123211

Herlyn Werner Wunderlich Syndrome with Hematocolpos: An Unusual Case Report of Full Diagnostic Approach and Treatment.

Rohit Bhoil1, Ajay Ahluwalia1, Narvir Chauhan1.   

Abstract

Herlyn-Werner-Wunderlich (HWW) syndrome is an uncommon combined müllerian duct anomalies (MDAs) and mesonephric duct malformation of female urogenital tract characterized by uterus didelphys and obstructed hemi-vagina and ipsilateral renal agenesis (OHVIRA) syndrome. We present a rare and unusual case of this syndrome in a 19 year-old female who suffered from hypomenorrhoea and abdominal pain. She had an obstructed hemi-vagina on right side which led to marked distention of ipsilateral cervix, while proximal hemi-vagina compressed the contralateral side causing its partial obstruction resulting in hypomenorrhoea. Understanding the imaging findings of this rare condition is important for early diagnosis in order to prevent complications which may lead to infertility.

Entities:  

Keywords:  Amenorrhea; Dysmenorrhea; Hematocolpos; Infertility; Vagina

Year:  2016        PMID: 27123211      PMCID: PMC4845524          DOI: 10.22074/ijfs.2016.4779

Source DB:  PubMed          Journal:  Int J Fertil Steril        ISSN: 2008-0778


  10 in total

1.  Double uterus, blind hemivagina, and ipsilateral renal agenesis: 36 cases and long-term follow-up.

Authors:  G B Candiani; L Fedele; M Candiani
Journal:  Obstet Gynecol       Date:  1997-07       Impact factor: 7.661

2.  Herlyn-Werner-Wunderlich syndrome with pregnancy: a rare presentation.

Authors:  Ritu Rana; Shika Pasrija; Manju Puri
Journal:  Congenit Anom (Kyoto)       Date:  2008-09       Impact factor: 1.409

3.  Müllerian anomalies: a proposed classification. (An analysis of 144 cases).

Authors:  V C Buttram; W E Gibbons
Journal:  Fertil Steril       Date:  1979-07       Impact factor: 7.329

Review 4.  Asymmetric lateral distribution of obstructed hemivagina and renal agenesis in women with uterus didelphys: institutional case series and a systematic literature review.

Authors:  Paolo Vercellini; Raffaella Daguati; Edgardo Somigliana; Paola Viganò; Annamaria Lanzani; Luigi Fedele
Journal:  Fertil Steril       Date:  2007-04       Impact factor: 7.329

5.  Management and outcome of patients with combined vaginal septum, bifid uterus, and ipsilateral renal agenesis (Herlyn-Werner-Wunderlich syndrome).

Authors:  Suad Gholoum; Pramod S Puligandla; Thomas Hui; Wendy Su; Elsa Quiros; Jean-Martin Laberge
Journal:  J Pediatr Surg       Date:  2006-05       Impact factor: 2.545

6.  Uterus didelphys with obstructed right hemivagina, ipsilateral renal agenesis and right pyocolpos: a case report.

Authors:  Hansa Dhar; Yasser A Razek; Ilham Hamdi
Journal:  Oman Med J       Date:  2011-11

7.  Double uterus with obstructed hemivagina and ipsilateral renal agenesis: pelvic anatomic variants in 87 cases.

Authors:  L Fedele; F Motta; G Frontino; E Restelli; S Bianchi
Journal:  Hum Reprod       Date:  2013-03-26       Impact factor: 6.918

8.  Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases.

Authors:  Cinzia Orazi; M Chiara Lucchetti; Paolo M S Schingo; Paola Marchetti; Fabio Ferro
Journal:  Pediatr Radiol       Date:  2007-05-15

9.  OHVIRA: Uterus didelphys, blind hemivagina and ipsilateral renal agenesis: Advantage MRI.

Authors:  Sunil K Bajaj; Ritu Misra; Brij B Thukral; Rohini Gupta
Journal:  J Hum Reprod Sci       Date:  2012-01

10.  Uterus didelphys with unilateral obstructed hemivagina with hematometrocolpos and hematosalpinx with ipsilateral renal agenesis.

Authors:  Gaurav Jindal; Satish Kachhawa; G L Meena; Gopal Dhakar
Journal:  J Hum Reprod Sci       Date:  2009-07
  10 in total
  3 in total

1.  Acute abdomen: Unusual presentation of Herlyn-Werner Wunderlich syndrome.

Authors:  Aysha Saleh; Maryam Alrashid; Saeed Al Hindi
Journal:  Int J Surg Case Rep       Date:  2021-04-27

2.  Case Report: A Rare Cause of Complicated Urinary Tract Infection in a Woman with Herlyn-Werner-Wunderlich Syndrome.

Authors:  Jun-Li Tsai; Shang-Feng Tsai
Journal:  Iran Red Crescent Med J       Date:  2016-10-30       Impact factor: 0.611

3.  Diagnosis and Treatment in a Tertiary Hospital of a Series of Complex Genital Malformations Corresponding to Double Uterus with Obstructed Hemivagina and Ipsilateral Renal Agenesis.

Authors:  Júlia Kefalás Troncon; Júlio César Rosa-E-Silva; Rayssa Miranda; Francisco José Candido-Dos-Reis; Omero Benedicto Poli-Neto; Antônio Alberto Nogueira
Journal:  Int J Reprod Med       Date:  2018-12-02
  3 in total

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