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Literature DB >> 27090552

Von Meyenburg complex and complete ductal plate malformation along with Klatskin tumour: a rare association.

Ashish Gupta¹, Bramhadatta Pattnaik¹, Ashim Das², Lileswar Kaman³.

Abstract

Von Meyenburg complexes (VMCs), or bile duct microhamartomas, are among the constellation of defects of ductal plate malformation. These present as multiple small intrahepatic cysts and are diagnosed incidentally. Association of intrahepatic VMCs with a bile duct cancer has rarely been reported. We describe a case of a 53-year-old man presenting with obstructive jaundice. Biochemistry and radiology gave a provisional diagnosis of a resectable Klatskin tumour. The patient underwent right hepatectomy with common bile duct and caudate lobe excision. The histopathological examination demonstrated intrahepatic VMCs with complete ductal malformation and malignancy at the hilum. 2016 BMJ Publishing Group Ltd.

Entities: Disease Species

Mesh：

Year: 2016 PMID： 27090552 PMCID： PMC4840689 DOI： 10.1136/bcr-2016-215220

Source DB: PubMed Journal: BMJ Case Rep ISSN： 1757-790X

13 in total

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Authors: D Jain; V R Sarode; F W Abdul-Karim; R Homer; M E Robert
Journal: Am J Surg Pathol Date: 2000-08 Impact factor: 6.394

2. Imaging findings of biliary hamartomas.

Authors: Rong-Qin Zheng; Bo Zhang; Masatoshi Kudo; Hirokazu Onda; Tatsuo Inoue
Journal: World J Gastroenterol Date: 2005-10-28 Impact factor: 5.742

3. The clinical presentation of Von Meyenburg complexes.

Authors: E Sinakos; L Papalavrentios; D Chourmouzi; D Dimopoulou; A Drevelegas; E Akriviadis
Journal: Hippokratia Date: 2011-04 Impact factor: 0.471

4. A case with intrahepatic double cancer: hepatocellular carcinoma and cholangiocarcinoma associated with multiple von Meyenburg complexes.

Authors: Y W Kim; Y K Park; J H Park; J Lee; S M Lee; S W Hong; M H Yang
Journal: Yonsei Med J Date: 1999-10 Impact factor: 2.759

5. Bile duct hamartomas. A report of two cases.

Authors: S C Wei; G T Huang; C H Chen; J C Sheu; Y M Tsang; H C Hsu; D S Chen
Journal: J Clin Gastroenterol Date: 1997-12 Impact factor: 3.062

Review 6. Imaging features of ductal plate malformations in adults.

Authors: N Venkatanarasimha; R Thomas; E M Armstrong; J F Shirley; B M Fox; S A Jackson
Journal: Clin Radiol Date: 2011-08-15 Impact factor: 2.350

7. Extra-hepatic bile duct hamartoma in a 10-month-old with a morgagni hernia and multiple anatomical anomalies: a rare and incidental finding.

Authors: Adil A Shah; Michael Karass; Andrew J Page; Bahig M Shehata; Megan M Durham
Journal: Pediatr Surg Int Date: 2013-03-02 Impact factor: 1.827

Von Meyenburg complex and complete ductal plate malformation along with Klatskin tumour: a rare association.

Review 1. Evidence for the neoplastic transformation of Von-Meyenburg complexes.

2. Imaging findings of biliary hamartomas.

3. The clinical presentation of Von Meyenburg complexes.

4. A case with intrahepatic double cancer: hepatocellular carcinoma and cholangiocarcinoma associated with multiple von Meyenburg complexes.

5. Bile duct hamartomas. A report of two cases.

Review 6. Imaging features of ductal plate malformations in adults.

7. Extra-hepatic bile duct hamartoma in a 10-month-old with a morgagni hernia and multiple anatomical anomalies: a rare and incidental finding.

8. Bile duct hamartomas (von Mayenburg complexes) mimicking liver metastases from bile duct cancer: MRC findings.

9. Biliary hamartomas (von Meyenburg complexes) in liver needle biopsies.

10. Cholangiocarcinoma arising in von Meyenburg complexes: report of four cases.

1. Surgery is the preferred treatment for bile duct hamartomas.

Review 2. Biliary Duct Hamartomas: A Systematic Review.