S Evans1, Z Khan1,2, L Jeys1, R Grimer1. 1. Royal Orthopaedic Hospital NHS Foundation Trust , UK. 2. Rehman Medical Institute , Pakistan.
Abstract
INTRODUCTION: A chordoma is a slow growing malignant tumour of notochordal origin. A tumour with histological features that are identical to those of a chordoma may arise outside the axial skeleton. To date, there is little in the literature documenting their clinical course. METHODS: Our large orthopaedic oncology database was used to document the clinical course of extra-axial chordoma. RESULTS: Over a 30-year period, 131 patients diagnosed with a chordoma were treated at our unit. Only three (2.3%) of these cases were extra-axial chordomas: one in the femur, one in the ulna and one in the proximal fibula. All underwent surgical resection. CONCLUSIONS: In view of the rarity of this tumour and the difficulty in confirming its diagnosis, we suggest that any suspected case is discussed with a specialist sarcoma multidisciplinary team so that the correct diagnosis can be achieved and treatment tailored accordingly.
INTRODUCTION:A chordoma is a slow growing malignant tumour of notochordal origin. A tumour with histological features that are identical to those of a chordoma may arise outside the axial skeleton. To date, there is little in the literature documenting their clinical course. METHODS: Our large orthopaedic oncology database was used to document the clinical course of extra-axial chordoma. RESULTS: Over a 30-year period, 131 patients diagnosed with a chordoma were treated at our unit. Only three (2.3%) of these cases were extra-axial chordomas: one in the femur, one in the ulna and one in the proximal fibula. All underwent surgical resection. CONCLUSIONS: In view of the rarity of this tumour and the difficulty in confirming its diagnosis, we suggest that any suspected case is discussed with a specialist sarcoma multidisciplinary team so that the correct diagnosis can be achieved and treatment tailored accordingly.
Authors: Alexander G Hadjipavlou; George M Kontakis; John N Gaitanis; Pavlos G Katonis; Philip Lander; Wayne N Crow Journal: Clin Orthop Relat Res Date: 2003-06 Impact factor: 4.176
Authors: S Boriani; F Chevalley; J N Weinstein; R Biagini; L Campanacci; F De Iure; P Piccill Journal: Spine (Phila Pa 1976) Date: 1996-07-01 Impact factor: 3.468