Literature DB >> 27077548

Pulmonary arterial hypertension associated with hereditary hemorrhagic telangiectasia successfully treated with sildenafil.

Ryo Miyake1, Takeo Fujino2, Kohtaro Abe1, Kazuya Hosokawa1, Kisho Ohtani1, Hiroko Morisaki3, Osamu Yamada4, Taiki Higo1, Tomomi Ide1.   

Abstract

Entities:  

Keywords:  ACVRL1 gene mutation; Hereditary hemorrhagic telangiectasia; Pulmonary arterial hypertension; Sildenafil

Mesh:

Substances:

Year:  2016        PMID: 27077548     DOI: 10.1016/j.ijcard.2016.03.211

Source DB:  PubMed          Journal:  Int J Cardiol        ISSN: 0167-5273            Impact factor:   4.164


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  5 in total

Review 1.  Cardiac and Hemodynamic Manifestations of Hereditary Hemorrhagic Telangiectasia.

Authors:  Ahmed Farhan; Muhammad A Latif; Anum Minhas; Clifford R Weiss
Journal:  Int J Angiol       Date:  2022-07-09

2.  Pulmonary Hypertension and Hereditary Hemorrhagic Telangiectasia Related to an ACVRL1 Mutation.

Authors:  Tetsuro Yokokawa; Koichi Sugimoto; Yusuke Kimishima; Tomofumi Misaka; Akiomi Yoshihisa; Hiroko Morisaki; Osamu Yamada; Kazuhiko Nakazato; Takafumi Ishida; Yasuchika Takeishi
Journal:  Intern Med       Date:  2019-09-11       Impact factor: 1.271

3.  Pulmonary arterial hypertension associated with pulmonary arteriovenous malformations and pulmonary veno-occlusive disease: A devastating combination.

Authors:  Baukje M Zaaijer; Nienke Duppen; Brigitte W M Willemse; Martijn V Verhagen; Marcus T R Roofthooft; Wim Timens; Rolf M F Berger; Johannes M Douwes
Journal:  Respir Med Case Rep       Date:  2021-12-01

4.  The clinical characteristics and long-term prognosis of pulmonary arterial hypertension associated with hereditary hemorrhagic telangiectasia.

Authors:  Wen Li; Chang-Ming Xiong; Qing Gu; Xiao-Tong Wang; Xiao-Ling Cheng; Li Huang; Tao Yang; Qin Luo; Zhi-Hui Zhao; Xin-Hai Ni; Zhi-Hong Liu; Jian-Guo He
Journal:  Pulm Circ       Date:  2018-02-26       Impact factor: 3.017

Review 5.  Pulmonary Arterial Hypertension and Hereditary Haemorrhagic Telangiectasia.

Authors:  Veronique M M Vorselaars; Anna E Hosman; Cornelis J J Westermann; Repke J Snijder; Johannes J Mager; Marie-Jose Goumans; Marco C Post
Journal:  Int J Mol Sci       Date:  2018-10-17       Impact factor: 5.923

  5 in total

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