Literature DB >> 26913981

Clonal Replacement Underlies Spontaneous Remission in Paroxysmal Nocturnal Haemoglobinuria.

Daria V Babushok1,2, Natasha Stanley2, Hongbo M Xie3, Hugh Huang2, Adam Bagg4, Timothy S Olson2,5, Monica Bessler1,2.   

Abstract

Entities:  

Keywords:  clonal evolution; clonal haematopoiesis; myelodysplastic syndrome; paroxysmal nocturnal haemoglobinuria; spontaneous remission

Mesh:

Year:  2016        PMID: 26913981      PMCID: PMC5446267          DOI: 10.1111/bjh.13963

Source DB:  PubMed          Journal:  Br J Haematol        ISSN: 0007-1048            Impact factor:   6.998


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  9 in total

1.  N-glycosylation bidirectionally extends the boundaries of thymocyte positive selection by decoupling Lck from Ca²⁺ signaling.

Authors:  Raymond W Zhou; Haik Mkhikian; Ani Grigorian; Amanda Hong; David Chen; Araz Arakelyan; Michael Demetriou
Journal:  Nat Immunol       Date:  2014-09-28       Impact factor: 25.606

Review 2.  Paroxysmal nocturnal haemoglobinuria: clinical manifestations, haematology, and nature of the disease.

Authors:  J V Dacie; S M Lewis
Journal:  Ser Haematol       Date:  1972

3.  Prolonged survival in paroxysmal nocturnal hemoglobinuria.

Authors:  S Charache
Journal:  Blood       Date:  1969-06       Impact factor: 22.113

4.  Emergence of clonal hematopoiesis in the majority of patients with acquired aplastic anemia.

Authors:  Daria V Babushok; Nieves Perdigones; Juan C Perin; Timothy S Olson; Wenda Ye; Jacquelyn J Roth; Curt Lind; Carine Cattier; Yimei Li; Helge Hartung; Michele E Paessler; Dale M Frank; Hongbo M Xie; Shanna Cross; Joshua D Cockroft; Gregory M Podsakoff; Dimitrios Monos; Jaclyn A Biegel; Philip J Mason; Monica Bessler
Journal:  Cancer Genet       Date:  2015-02-02

5.  Acute leukaemia in paroxysmal nocturnal haemoglobinuria. Case report and review of the literature.

Authors:  F Cornélis; L Montfort; J C Osselaer; A Sonet; C Doyen; C Chatelain; B Chatelain; A Bosly
Journal:  Hematol Cell Ther       Date:  1996-07

6.  Paroxysmal nocturnal hemoglobinuria after autologous stem cell transplantation: extinction of the clone during treatment with eculizumab - pathophysiological implications of a unique clinical case.

Authors:  Stefano Pulini; Ludovica Marando; Annalisa Natale; Caterina Pascariello; Virginia Catinella; Luigi Del Vecchio; Antonio M Risitano; Giuseppe Fioritoni
Journal:  Acta Haematol       Date:  2011-05-19       Impact factor: 2.195

7.  Neutral evolution in paroxysmal nocturnal hemoglobinuria.

Authors:  David Dingli; Lucio Luzzatto; Jorge M Pacheco
Journal:  Proc Natl Acad Sci U S A       Date:  2008-11-14       Impact factor: 11.205

8.  Deep sequencing reveals stepwise mutation acquisition in paroxysmal nocturnal hemoglobinuria.

Authors:  Wenyi Shen; Michael J Clemente; Naoko Hosono; Kenichi Yoshida; Bartlomiej Przychodzen; Tetsuichi Yoshizato; Yuichi Shiraishi; Satoru Miyano; Seishi Ogawa; Jaroslaw P Maciejewski; Hideki Makishima
Journal:  J Clin Invest       Date:  2014-09-17       Impact factor: 14.808

9.  Natural history of paroxysmal nocturnal hemoglobinuria.

Authors:  P Hillmen; S M Lewis; M Bessler; L Luzzatto; J V Dacie
Journal:  N Engl J Med       Date:  1995-11-09       Impact factor: 91.245

  9 in total
  10 in total

1.  Battle of the clones: paroxysmal nocturnal hemoglobinuria vs myelodysplastic syndrome.

Authors:  Chloé Friedrich; Juliette Gay; Anne-Sophie Alary; Jean-Benoît Arlet; Gérard Socie; Véronique Fremaux-Bacchi; Isabelle Radford Weiss; Olivier Kosmider; Luc Darnige
Journal:  Ann Hematol       Date:  2020-06-13       Impact factor: 3.673

2.  Secondary myelodysplastic syndrome and leukemia in acquired aplastic anemia and paroxysmal nocturnal hemoglobinuria.

Authors:  Lova Sun; Daria V Babushok
Journal:  Blood       Date:  2020-07-02       Impact factor: 22.113

3.  The predictive value of PNH clones, 6p CN-LOH, and clonal TCR gene rearrangement for aplastic anemia diagnosis.

Authors:  Yash B Shah; Salvatore F Priore; Yimei Li; Chi N Tang; Peter Nicholas; Peter Kurre; Timothy S Olson; Daria V Babushok
Journal:  Blood Adv       Date:  2021-08-24

Review 4.  Paroxysmal nocturnal haemoglobinuria.

Authors:  Anita Hill; Amy E DeZern; Taroh Kinoshita; Robert A Brodsky
Journal:  Nat Rev Dis Primers       Date:  2017-05-18       Impact factor: 52.329

5.  Spontaneous Remission in Paroxysmal Nocturnal Hemoglobinuria: An Extremely Rare Case

Authors:  Özgür Mehta; Ayfer Gedük
Journal:  Turk J Haematol       Date:  2022-02-18       Impact factor: 2.029

6.  Spontaneous Remission in Paroxysmal Nocturnal Hemoglobinuria-Return to Health or Transition Into Malignancy?

Authors:  Eva-Stina Korkama; Anna-Elina Armstrong; Hanna Jarva; Seppo Meri
Journal:  Front Immunol       Date:  2018-08-02       Impact factor: 7.561

7.  Evolutionary dynamics of paroxysmal nocturnal hemoglobinuria.

Authors:  Nathaniel Mon Père; Tom Lenaerts; Jorge M Pacheco; David Dingli
Journal:  PLoS Comput Biol       Date:  2018-06-18       Impact factor: 4.475

8.  Hodgkin lymphoma patients have an increased incidence of idiopathic acquired aplastic anemia.

Authors:  Taylor Linaburg; Adam R Davis; Noelle V Frey; Muhammad R Khawaja; Daniel J Landsburg; Stephen J Schuster; Jakub Svoboda; Yimei Li; Yuliya Borovskiy; Timothy S Olson; Adam Bagg; Elizabeth O Hexner; Daria V Babushok
Journal:  PLoS One       Date:  2019-04-05       Impact factor: 3.240

9.  Is nature truly healing itself? Spontaneous remissions in Paroxysmal Nocturnal Hemoglobinuria.

Authors:  Carmelo Gurnari; Simona Pagliuca; Tariq Kewan; Waled Bahaj; Minako Mori; Bhumika J Patel; Valeria Visconte; Jaroslaw P Maciejewski
Journal:  Blood Cancer J       Date:  2021-11-27       Impact factor: 11.037

Review 10.  Managing Fatigue in Patients with Paroxysmal Nocturnal Hemoglobinuria: A Patient-Focused Perspective.

Authors:  Bruno Fattizzo; Francesca Cavallaro; Esther Natalie Oliva; Wilma Barcellini
Journal:  J Blood Med       Date:  2022-06-17
  10 in total

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