Literature DB >> 26873708

Life with a Primary Immune Deficiency: a Systematic Synthesis of the Literature and Proposed Research Agenda.

Morgan N Similuk1, Angela Wang2, Michael J Lenardo3, Lori H Erby4.   

Abstract

PURPOSE: The clinical immunology literature is punctuated with research on psychosocial dimensions of illness. Studies investigating the lived experiences and stated needs of patients with primary immune deficiencies and their families are essential to improving clinical management and determining the research questions that matter to patients and other stakeholders. Yet, to move the field forward, a systematic review of literature and proposed agenda is needed.
METHODS: A systematic review was conducted via PubMed and Scopus to include original research on psychological, social, or behavioral aspects of primary immune deficiencies published between 1999 and 2015. A Title/Abstract keyword search was conducted, 317 candidate article abstracts were manually reviewed, and forward/backward reference searches were completed.
RESULTS: Twenty-nine studies met inclusion criteria. These illuminate the complex psychological, social, and emotional experiences of primary immune deficiency. Themes included the potential for negative psychosocial impact from disease; adaptation over time; the multi-dimensional assessments of quality of life; familial impact; the important roles of hope, developing a sense of control, social support; and addressing anxiety/depression in our patients and their families. Methodological considerations and areas for improvement are discussed.
CONCLUSION: We propose the research agenda focus on study creativity and rigor, with improved engagement with existing literature and critical study design (e.g., methodology with adequate statistical power, careful variable selection, etc.). This review highlights opportunities to advance psychosocial research and bring a brighter future to clinicians, researchers, and families affected by primary immune deficiency.

Entities:  

Keywords:  Quality of life; patient-centered; primary immune deficiency; psychosocial

Mesh:

Year:  2016        PMID: 26873708     DOI: 10.1007/s10875-016-0241-1

Source DB:  PubMed          Journal:  J Clin Immunol        ISSN: 0271-9142            Impact factor:   8.317


  45 in total

1.  Health-related quality of life (HRQL) in immunodeficient adults with selective IgA deficiency compared with age- and gender-matched controls and identification of risk factors for poor HRQL.

Authors:  G H Jörgensen; A Gardulf; M I Sigurdsson; S Arnlaugsson; L Hammarström; B R Ludviksson
Journal:  Qual Life Res       Date:  2014-03       Impact factor: 4.147

Review 2.  Home-based subcutaneous immunoglobulin versus hospital-based intravenous immunoglobulin in treatment of primary antibody deficiencies: systematic review and meta analysis.

Authors:  Hassan Abolhassani; Mohammad Salehi Sadaghiani; Asghar Aghamohammadi; Hans D Ochs; Nima Rezaei
Journal:  J Clin Immunol       Date:  2012-06-23       Impact factor: 8.317

3.  Parents' experiences one year on from their child's hematopoietic stem cell transplant for primary immunodeficiency.

Authors:  Elizabeth McDowell; Penny Titman; Sarah Davidson
Journal:  J Health Psychol       Date:  2010-07-08

4.  Impact of BRCA1/BRCA2 mutation testing on psychologic distress in a clinic-based sample.

Authors:  Marc D Schwartz; Beth N Peshkin; Chanita Hughes; David Main; Claudine Isaacs; Caryn Lerman
Journal:  J Clin Oncol       Date:  2002-01-15       Impact factor: 44.544

Review 5.  Evaluating health-related quality-of-life studies in paediatric populations: some conceptual, methodological and developmental considerations and recent applications.

Authors:  Mirella De Civita; Dean Regier; Abul H Alamgir; Aslam H Anis; Mark J Fitzgerald; Carlo A Marra
Journal:  Pharmacoeconomics       Date:  2005       Impact factor: 4.981

6.  Quality of life in common variable immunodeficiency requiring intravenous immunoglobulin therapy.

Authors:  Haig Tcheurekdjian; Tonya Palermo; Robert Hostoffer
Journal:  Ann Allergy Asthma Immunol       Date:  2004-08       Impact factor: 6.347

7.  22q11.2 deletion syndrome: behaviour problems of children and adolescents and parental stress.

Authors:  W Briegel; M Schneider; K Otfried Schwab
Journal:  Child Care Health Dev       Date:  2008-09-10       Impact factor: 2.508

8.  Managing space and marking time: mothering severely ill infants in hospital isolation.

Authors:  Patricia McKeever; Sally O'Neill; Karen-Lee Miller
Journal:  Qual Health Res       Date:  2002-10

9.  Coping, quality of life, and hope in adults with primary antibody deficiencies.

Authors:  Hanne Marie Høybråten Sigstad; Asbjørg Stray-Pedersen; Stig S Frøland
Journal:  Health Qual Life Outcomes       Date:  2005-05-04       Impact factor: 3.186

10.  Quality of life in children with primary antibody deficiency.

Authors:  P Titman; Z Allwood; C Gilmour; C Malcolmson; C Duran-Persson; C Cale; G Davies; H Gaspar; A Jones
Journal:  J Clin Immunol       Date:  2014-07-09       Impact factor: 8.317

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  1 in total

1.  Provider Perceptions of Quality of Life, Neurocognition, Physical Well-being, and Psychosocial Health in Patients with Primary Immunodeficiency/Immune Dysregulation Conditions.

Authors:  Thomas F Michniacki; Kelly J Walkovich; Lauren E Merz; Julie Sturza; Roshini S Abraham
Journal:  J Clin Immunol       Date:  2019-10-26       Impact factor: 8.317

  1 in total

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