Literature DB >> 26740675

Channelopathy-related SCN10A gene variants predict cerebellar dysfunction in multiple sclerosis.

Tina Roostaei1, Shokufeh Sadaghiani1, Min Tae M Park1, Rahil Mashhadi1, Aria Nazeri1, Sina Noshad1, Mohammad Javad Salehi1, Maryam Naghibzadeh1, Abdorreza Naser Moghadasi1, Mahsa Owji1, Rozita Doosti1, Amir Pejman Hashemi Taheri1, Ali Shakouri Rad1, Amirreza Azimi1, M Mallar Chakravarty1, Aristotle N Voineskos1, Arash Nazeri2, Mohammad Ali Sahraian2.   

Abstract

OBJECTIVE: To determine the motor-behavioral and neural correlates of putative functional common variants in the sodium-channel NaV1.8 encoding gene (SCN10A) in vivo in patients with multiple sclerosis (MS).
METHODS: We recruited 161 patients with relapsing-onset MS and 94 demographically comparable healthy participants. All patients with MS underwent structural MRI and clinical examinations (Expanded Disability Status Scale [EDSS] and Multiple Sclerosis Functional Composite [MSFC]). Whole-brain voxel-wise and cerebellar volumetry were performed to assess differences in regional brain volumes between genotype groups. Resting-state fMRI was acquired from 62 patients with MS to evaluate differences in cerebellar functional connectivity. All participants were genotyped for 4 potentially functional SCN10A polymorphisms.
RESULTS: Two SCN10A polymorphisms in high linkage disequilibrium (r(2) = 0.95) showed significant association with MSFC performance in patients with MS (rs6795970: p = 6.2 × 10(-4); rs6801957: p = 0.0025). Patients with MS with rs6795970(AA) genotype performed significantly worse than rs6795970(G) carriers in MSFC (p = 1.8 × 10(-4)) and all of its subscores. This association was independent of EDSS and cerebellar atrophy. Although the genotype groups showed no difference in regional brain volumes, rs6795970(AA) carriers demonstrated significantly diminished cerebellar functional connectivity with the thalami and midbrain. No significant SCN10A-genotype effect was observed on MSFC performance in healthy participants.
CONCLUSIONS: Our data suggest that SCN10A variation substantially influences functional status, including prominent effects on motor coordination in patients with MS. These findings were supported by the effects of this variant on a neural system important for motor coordination, namely cerebello-thalamic circuitry. Overall, our findings add to the emerging evidence that suggests that sodium channel NaV1.8 could serve as a target for future drug-based interventions to treat cerebellar dysfunction in MS.
© 2016 American Academy of Neurology.

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Year:  2016        PMID: 26740675      PMCID: PMC4773947          DOI: 10.1212/WNL.0000000000002326

Source DB:  PubMed          Journal:  Neurology        ISSN: 0028-3878            Impact factor:   9.910


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