Literature DB >> 26650462

Torticollis in a haemophilic infant with inhibitor: a case of spinal epidural haematoma.

Yesim Oymak1, Neryal Muminoglu, Yilmaz Ay, Tuba H Karapinar, Sultan A Köker, Ersin Töret, Aşiyan K Ylmaz, Müge Gürçnar, Canan Vergin.   

Abstract

Central nervous system bleeding, which can be a life-threatening complication, is seen in 2.7% of patients with haemophilia. Spinal epidural haematomas represent about one-tenth of such cases. Here, we report on a 10-month-old boy with severe haemophilia A, who presented with torticollis. Although administration of factor VIII at a dose of 50 U/kg, the patient developed flaccid paralysis of the upper extremities. Factor VIII inhibitor screen was positive. Magnetic resonance imaging of the spine revealed spinal epidural haematomas, extending from C-1 to the cauda equina. Treatment was continued with recombinant activated factor VIIa without surgery. After 1 month, complete neurological recovery was achieved and fully resolved haematomas were detected on spinal MRI. A prompt radiological evaluation of the cervical spine with MRI should be made in patients with haemophilia presenting with torticollis. In addition, in the case of life-threatening bleeding in patients with haemophilia, the possibility of an inhibitor should be kept in mind.

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Year:  2016        PMID: 26650462     DOI: 10.1097/MBC.0000000000000465

Source DB:  PubMed          Journal:  Blood Coagul Fibrinolysis        ISSN: 0957-5235            Impact factor:   1.276


  1 in total

1.  Conservative therapy for spinal epidural hematoma in a child with hemophilia A with high-titer VIII inhibitors.

Authors:  Guige Wang; Shengru Wang
Journal:  J Int Med Res       Date:  2021-02       Impact factor: 1.671

  1 in total

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