Literature DB >> 26640568

Aplasia cutis congenita: A case report and literature review.

Xunhong Duan1, G E Yang2, Dongqi Yu1, Changlong Yu1, Biao Wang1, Yibin Guo1.   

Abstract

Aplasia cutis congenita (ACC) is a rare condition with an unclear pathogenic mechanism, although the condition has been suggested to occur as a result of the disrupted development or degeneration of skin in utero. ACC associated with fetus papyraceus has been described in numerous studies. Although there have been several reports of ACC, surgical treatment of ACC using the head as a site of donor skin is rarely reported. The present study describes the case of a 1-week-old patient with ACC that was healed by skin grafting, using the scalp as the donor site. The outcome of the procedure showed that the use of the scalp as a donor skin site for grafting is an effective treatment for large and deep ACC lesions arising on sites other than the head.

Entities:  

Keywords:  aplasia cutis congenita; infant; skin graft; treatment

Year:  2015        PMID: 26640568      PMCID: PMC4665749          DOI: 10.3892/etm.2015.2737

Source DB:  PubMed          Journal:  Exp Ther Med        ISSN: 1792-0981            Impact factor:   2.447


  12 in total

1.  Aplasia cutis congenita of the trunk with fetus papyraceus.

Authors:  Benjamin J Kelly; Nancy J Samolitis; Don-Ling Xie; Robert A Skidmore
Journal:  Pediatr Dermatol       Date:  2002 Jul-Aug       Impact factor: 1.588

2.  Conservative treatment of cutis aplasia.

Authors:  A Wexler; M Harris; M Lesavoy
Journal:  Plast Reconstr Surg       Date:  1990-12       Impact factor: 4.730

3.  Aplasia cutis congenita: Successful conservative treatment.

Authors:  Georgia Skoufi; Georgios Lialios; Nikolas Plachouras; Demetrios Kutsogiannis; Alexandros Mperis
Journal:  Pediatr Int       Date:  2006-10       Impact factor: 1.524

4.  Aplasia cutis congenita with hair collar sign and dermal melanocytosis.

Authors:  Ah-Young Cho; Sang-Sin Lee; Young Lee; Chang-Deok Kim; Jeung-Hoon Lee; Young-Joon Seo
Journal:  Int J Dermatol       Date:  2011-02-23       Impact factor: 2.736

5.  Symmetric aplasia cutis congenita associated with fetus papyraceus: report of two cases.

Authors:  Rhonda Quain Klein; Deanne Mraz Robinson; Colette D Lieber; Richard J Antaya
Journal:  Pediatr Dermatol       Date:  2011-03-25       Impact factor: 1.588

6.  Aplasia cutis congenita of the trunk and scalp associated with fetus papyraceus.

Authors:  Marie-Michèle Blouin; Jean Bernard; Francine Caron; Isabelle Auger
Journal:  Int J Dermatol       Date:  2011-06       Impact factor: 2.736

7.  Aplasia cutis congenita in a setting of fetus papyraceus associated with small fetal abdominal circumference and high alpha-fetoprotein and amniotic acetylcholinesterase.

Authors:  Joni M Mazza; Janice F Klein; Kurt Christopher; Nanette B Silverberg
Journal:  Pediatr Dermatol       Date:  2013-10-11       Impact factor: 1.588

Review 8.  Aplasia cutis congenita: a clinical review and proposal for classification.

Authors:  I J Frieden
Journal:  J Am Acad Dermatol       Date:  1986-04       Impact factor: 11.527

9.  Symmetric truncal aplasia cutis congenita following multifetal reduction of a sextuplet pregnancy.

Authors:  Julie V Schaffer; Dorota A Popiolek; Seth J Orlow
Journal:  J Pediatr       Date:  2008-12       Impact factor: 4.406

Review 10.  Aplasia cutis congenita with fetus papyraceus: report and review of the literature.

Authors:  Therdpong Tempark; Tor A Shwayder
Journal:  Int J Dermatol       Date:  2012-12       Impact factor: 2.736

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  5 in total

1.  Aplasia cutis congenita and amniotic band syndrome: an uncommon association.

Authors:  Joana Pimenta; Patrícia Lapa; Lina Ramos
Journal:  BMJ Case Rep       Date:  2017-01-31

2.  Extreme aplasia cutis congenita involving the skull.

Authors:  Sebastian Shrager; Vlad Voin; Joe Iwanaga; R Shane Tubbs; James Johnston
Journal:  Childs Nerv Syst       Date:  2017-05-05       Impact factor: 1.475

3.  Aplasia cutis congenita: Two case reports and discussion of the literature.

Authors:  Alexandros Blionas; Dimitrios Giakoumettis; Elias Antoniades; Evangelos Drosos; Andreas Mitsios; Sotirios Plakas; Georgios Sfakianos; Marios S Themistocleous
Journal:  Surg Neurol Int       Date:  2017-11-09

Review 4.  Multiple aplasia cutis congenita type V and fetus papyraceous: a case report and review of the literature.

Authors:  V Thadchanamoorthy; Kavinda Dayasiri; M Thirukumar; N Thamilvannan; S H Chandraratne
Journal:  J Med Case Rep       Date:  2021-03-04

5.  Aplasia Cutis Congenita: A Case Report.

Authors:  Tahani Magliah; Faiza Alghamdi
Journal:  Case Rep Dermatol       Date:  2018-07-05
  5 in total

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