| Literature DB >> 26640227 |
Cecile Thomas-Teinturier1, Arrate Pereda2, Intza Garin2, Ignacio Diez-Lopez3, Agnès Linglart1,4,5, Caroline Silve4,6, Guiomar Pérez de Nanclares2.
Abstract
Autosomal-dominant brachydactyly type E is a congenital limb malformation characterized by small hands and feet as a result of shortened metacarpals and metatarsals. Alterations that predict haploinsufficiency of PTHLH, the gene coding for parathyroid hormone related protein (PTHrP), have been identified as a cause of this disorder in seven families. Here, we report three patients affected with brachydactyly type E, caused by PTHLH mutations expected to result in haploinsufficiency, and discuss our data compared to published reports.Entities:
Keywords: PTHLH; PTHrP; brachydactyly type E; short stature
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Year: 2015 PMID: 26640227 DOI: 10.1002/ajmg.a.37490
Source DB: PubMed Journal: Am J Med Genet A ISSN: 1552-4825 Impact factor: 2.802