| Literature DB >> 26616875 |
Colin Casault1, Katayoun Alikhani2, Neelan Pillay2, Marcus Koch3.
Abstract
This is a case of autoimmune encephalitis with features of faciobrachial dystonic seizures (FBDS) pathognomonic for Leucine Rich Glioma inactivated (LGI)1 antibody encephalitis. This voltage-gated potassium channel complex encephalitis is marked by rapid onset dementia, FBDS and hyponatremia, which is sensitive to management with immunotherapy including steroids, IVIG and other agents. In this case report we review the clinical features, imaging and management of this condition. CrownEntities:
Keywords: Faciobrachial dystonic seizures; LGI1 encephalitis; Limbic encephalitis; Paraneoplastic disease; Steroid sensitive encephalopathy
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Year: 2015 PMID: 26616875 DOI: 10.1016/j.jneuroim.2015.10.010
Source DB: PubMed Journal: J Neuroimmunol ISSN: 0165-5728 Impact factor: 3.478