Literature DB >> 26616875

Jerking & confused: Leucine-rich glioma inactivated 1 receptor encephalitis.

Colin Casault1, Katayoun Alikhani2, Neelan Pillay2, Marcus Koch3.   

Abstract

This is a case of autoimmune encephalitis with features of faciobrachial dystonic seizures (FBDS) pathognomonic for Leucine Rich Glioma inactivated (LGI)1 antibody encephalitis. This voltage-gated potassium channel complex encephalitis is marked by rapid onset dementia, FBDS and hyponatremia, which is sensitive to management with immunotherapy including steroids, IVIG and other agents. In this case report we review the clinical features, imaging and management of this condition. Crown
Copyright © 2015. Published by Elsevier B.V. All rights reserved.

Entities:  

Keywords:  Faciobrachial dystonic seizures; LGI1 encephalitis; Limbic encephalitis; Paraneoplastic disease; Steroid sensitive encephalopathy

Mesh:

Substances:

Year:  2015        PMID: 26616875     DOI: 10.1016/j.jneuroim.2015.10.010

Source DB:  PubMed          Journal:  J Neuroimmunol        ISSN: 0165-5728            Impact factor:   3.478


  6 in total

1.  LGI1 antibody encephalopathy overlapping with sporadic Creutzfeldt-Jakob disease.

Authors:  Boaz Kim; Patrick Yoo; Tom Sutherland; Alison Boyd; Christiane Stehmann; Catriona McLean; Steven Collins
Journal:  Neurol Neuroimmunol Neuroinflamm       Date:  2016-06-16

Review 2.  Antibody-LGI 1 autoimmune encephalitis manifesting as rapidly progressive dementia and hyponatremia: a case report and literature review.

Authors:  Xuanting Li; Junliang Yuan; Lei Liu; Wenli Hu
Journal:  BMC Neurol       Date:  2019-02-07       Impact factor: 2.474

3.  Clinical Features and Therapeutic Effects of Anti-leucine-rich Glioma Inactivated 1 Encephalitis: A Systematic Review.

Authors:  Yuou Teng; Ting Li; Zhizhong Yang; Mingwan Su; Jingnian Ni; Mingqing Wei; Jing Shi; Jinzhou Tian
Journal:  Front Neurol       Date:  2022-01-12       Impact factor: 4.003

Review 4.  Neuronal Surface Autoantibodies in Neuropsychiatric Disorders: Are There Implications for Depression?

Authors:  Shenghua Zong; Carolin Hoffmann; Marina Mané-Damas; Peter Molenaar; Mario Losen; Pilar Martinez-Martinez
Journal:  Front Immunol       Date:  2017-07-05       Impact factor: 7.561

Review 5.  Autoimmune encephalitis in psychiatric institutions: current perspectives.

Authors:  Chloe Bost; Olivier Pascual; Jérôme Honnorat
Journal:  Neuropsychiatr Dis Treat       Date:  2016-10-27       Impact factor: 2.570

6.  Case Report: Anti-LGI1 Encephalitis Following COVID-19 Vaccination.

Authors:  Yair Zlotnik; Avi Gadoth; Ibrahim Abu-Salameh; Anat Horev; Rosa Novoa; Gal Ifergane
Journal:  Front Immunol       Date:  2022-01-05       Impact factor: 7.561

  6 in total

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