| Literature DB >> 26593138 |
Dominique Valeyre1, Jean-François Bernaudin2, Florence Jeny3, Boris Duchemann4, Olivia Freynet4, Carole Planès5, Marianne Kambouchner6, Hilario Nunes3.
Abstract
Sarcoidosis is a systemic disease, with lung involvement in almost all cases. Abnormal chest radiography is usually a key step for considering diagnosis. Lung impact is investigated through imaging; pulmonary function; and, when required, 6-minute walk test, cardiopulmonary exercise testing, or right heart catheterization. There is usually a reduction of lung volumes, and forced vital capacity is the most accurate parameter to reflect the impact of pulmonary sarcoidosis with or without pulmonary infiltration at imaging. Various evolution patterns have been described. Increased risk of death is associated with advanced pulmonary fibrosis or cor pulmonale, particularly in African American patients.Entities:
Keywords: Evolution; Lung; Pathology; Pulmonary function; Sarcoidosis
Mesh:
Year: 2015 PMID: 26593138 DOI: 10.1016/j.ccm.2015.08.006
Source DB: PubMed Journal: Clin Chest Med ISSN: 0272-5231 Impact factor: 2.878