Literature DB >> 26510034

Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR.

Claire E Wainwright, J Stuart Elborn, Bonnie W Ramsey.   

Abstract

Entities:  

Mesh：

Substances：

Year:  2015        PMID： 26510034     DOI： 10.1056/NEJMc1510466

Source DB:  PubMed          Journal:  N Engl J Med        ISSN： 0028-4793            Impact factor:   91.245


× No keyword cloud information.
  72 in total

1.  Pregnancy among cystic fibrosis women in the era of CFTR modulators.

Authors:  Sonya L Heltshe; Emily M Godfrey; Tatiana Josephy; Moira L Aitken; Jennifer L Taylor-Cousar
Journal:  J Cyst Fibros       Date:  2017-02-10       Impact factor: 5.482

2.  Contribution of Cotranslational Folding Defects to Membrane Protein Homeostasis.

Authors:  Francis J Roushar; Timothy C Gruenhagen; Wesley D Penn; Bian Li; Jens Meiler; Beata Jastrzebska; Jonathan P Schlebach
Journal:  J Am Chem Soc       Date:  2018-12-26       Impact factor: 15.419

3.  Cystic Fibrosis: The Dawn of a New Therapeutic Era.

Authors:  Sonya L Heltshe; Jonathan Cogen; Kathleen J Ramos; Christopher H Goss
Journal:  Am J Respir Crit Care Med       Date:  2017-04-15       Impact factor: 21.405

Review 4.  Protein Degradation and the Pathologic Basis of Disease.

Authors:  John Hanna; Angel Guerra-Moreno; Jessie Ang; Yagmur Micoogullari
Journal:  Am J Pathol       Date:  2018-10-10       Impact factor: 4.307

Review 5.  Safety and efficacy of treatment with lumacaftor in combination with ivacaftor in younger patients with cystic fibrosis.

Authors:  Pi Chun Cheng; Stamatia Alexiou; Ronald C Rubenstein
Journal:  Expert Rev Respir Med       Date:  2019-04-08       Impact factor: 3.772

6.  Efficacy of lumacaftor-ivacaftor for the treatment of cystic fibrosis patients homozygous for the F508del-CFTR mutation.

Authors:  Deborah M Cholon; Charles R Esther; Martina Gentzsch
Journal:  Expert Rev Precis Med Drug Dev       Date:  2016-04-22

Review 7.  The CF gastrointestinal microbiome: Structure and clinical impact.

Authors:  Geraint B Rogers; Michael R Narkewicz; Lucas R Hoffman
Journal:  Pediatr Pulmonol       Date:  2016-10

8.  Perception of Pulmonary Function in Children with Asthma and Cystic Fibrosis.

Authors:  Erick Forno; Neethu Abraham; Daniel G Winger; Christian Rosas-Salazar; Geoffrey Kurland; Daniel J Weiner
Journal:  Pediatr Allergy Immunol Pulmonol       Date:  2018-09-17       Impact factor: 1.349

Review 9.  New Therapeutic Approaches to Modulate and Correct Cystic Fibrosis Transmembrane Conductance Regulator.

Authors:  Thida Ong; Bonnie W Ramsey
Journal:  Pediatr Clin North Am       Date:  2016-08       Impact factor: 3.278

10.  Folding and Misfolding of Human Membrane Proteins in Health and Disease: From Single Molecules to Cellular Proteostasis.

Authors:  Justin T Marinko; Hui Huang; Wesley D Penn; John A Capra; Jonathan P Schlebach; Charles R Sanders
Journal:  Chem Rev       Date:  2019-01-04       Impact factor: 60.622
View more

北京卡尤迪生物科技股份有限公司 © 2022-2023.