| Literature DB >> 26453627 |
J Stuart Elborn1, Scott C Bell2, Susan L Madge3, Pierre-Regis Burgel4, Carlo Castellani5, Steven Conway6, Karleen De Rijcke7, Birgit Dembski8, Pavel Drevinek9, Harry G M Heijerman10, J Alistair Innes11, Anders Lindblad12, Bruce Marshall13, Hanne V Olesen14, Andreas L Reimann15, Ampara Solé16, Laura Viviani17, Thomas O F Wagner18, Tobias Welte19, Francesco Blasi20.
Abstract
The improved survival in people with cystic fibrosis has led to an increasing number of patients reaching adulthood. This trend is likely to be maintained over the next decades, suggesting a need to increase the number of centres with expertise in the management of adult patients with cystic fibrosis. These centres should be capable of delivering multidisciplinary care addressing the complexity of the disease, in addition to addressing the psychological burden on patients and their families. Further issues that require attention are organ transplantation and end of life management.Lung disease in adults with cystic fibrosis drives most of the clinical care requirements, and major life-threatening complications, such as respiratory infection, respiratory failure, pneumothorax and haemoptysis, and the management of lung transplantation require expertise from trained respiratory physicians. The taskforce therefore strongly reccommends that medical leadership in multidisciplinary adult teams should be attributed to a respiratory physician adequately trained in cystic fibrosis management.The task force suggests the implementation of a core curriculum for trainees in adult respiratory medicine and the selection and accreditation of training centres that deliver postgraduate training to the standards of the HERMES programme.Entities:
Mesh:
Year: 2015 PMID: 26453627 DOI: 10.1183/13993003.00592-2015
Source DB: PubMed Journal: Eur Respir J ISSN: 0903-1936 Impact factor: 16.671