Literature DB >> 26362833

Bilateral Orbital IgG4-Related Disease with Systemic and Corneal Involvement Showing an Excellent Response to Steroid and Rituximab Therapy: Report of a Case with 11 Years Follow-Up.

Agnes I Berta1, Abbas Agaimy2, Joachim M Braun1, Bernhard Manger3, Friedrich E Kruse1, Leonard Holbach1.   

Abstract

IgG4-related disease is a newly recognized fibro-inflammatory condition. The purpose of this report is to present a patient with 11 years of follow-up, who revealed characteristic features of IgG4-related disease with systemic, orbital and corneal involvement and showed a favorable response to steroids and rituximab treatment.

Entities:  

Keywords:  Bilateral IgG4-related orbital disease; peripheral ulcerative keratitis; sclerosing autoimmune pancreatitis; steroid and rituximab treatment

Mesh：

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Year:  2015        PMID： 26362833     DOI： 10.3109/01676830.2015.1057290

Source DB:  PubMed          Journal:  Orbit        ISSN： 0167-6830


  2 in total

Review 1.  [Therapy options for malignant eyelid tumors].

Authors:  M Weiling; A Bergua; F E Kruse; L Holbach
Journal:  Ophthalmologe       Date:  2016-12       Impact factor: 1.059

2.  IgG4-related disease presenting with scarring alopecia of the scalp.

Authors:  Paul M Hoesly; Jason C Sluzevich
Journal:  JAAD Case Rep       Date:  2018-06-06
  2 in total

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