| Literature DB >> 26339456 |
Ziling Huang1, Shuai Li1, Yi Zhu2, Hailong Zhu1, Xianghua Yi1.
Abstract
Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a recently described rare condition, characterized by pleural and subpleural parenchymal fibrosis, predominantly in the upper lobes. The clinical course of this disease is progressive and prognosis is poor, with little information regarding the etiology of IIPPFE. This report describes an IPPFE patient with convincing evidence of inhalational dust and suggests that dust exposure should be considered as a new causative factor of IPPFE.Entities:
Keywords: Pleuroparenchymal fibroelastosis; dust exposure; idiopathic interstitial pneumonias
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Year: 2015 PMID: 26339456 PMCID: PMC4555784
Source DB: PubMed Journal: Int J Clin Exp Pathol ISSN: 1936-2625