Left main coronary artery embolization in an 11-year-old girl due to inflammatory myofibroblastic tumor of the mitral valve.

This report describes a rare case of a subtotal left main coronary artery occlusion from mitral valve tumor embolization in an 11-year-old African American girl. This case is the first to report isolated ST segment elevation in lead aVR as a sign of a subtotal left main coronary artery occlusion in the pediatric population. In our case, we report a rare case of inflammatory myofibroblastic tumor of the mitral valve presenting with acute myocardial infarction due to embolization into the left main coronary artery. Coronary intervention was successfully performed using an aspiration catheter. Inflammatory myofibroblastic tumor usually presents as a solitary pulmonary nodule. Intracardiac involvement has been rarely reported. Despite the benign nature of the tumor, fatal presentations can occur. Early recognition and rapid intervention can be lifesaving in these patients.