| Literature DB >> 26330554 |
Stephanie Santarriaga1, Amber Petersen2, Kelechi Ndukwe1, Anthony Brandt1, Nashaat Gerges2, Jamie Bruns Scaglione3, Kenneth Matthew Scaglione4.
Abstract
The expression, misfolding, and aggregation of long repetitive amino acid tracts are a major contributing factor in a number of neurodegenerative diseases, including C9ORF72 amyotrophic lateral sclerosis/frontotemporal dementia, fragile X tremor ataxia syndrome, myotonic dystrophy type 1, spinocerebellar ataxia type 8, and the nine polyglutamine diseases. Protein aggregation is a hallmark of each of these diseases. In model organisms, including yeast, worms, flies, mice, rats, and human cells, expression of proteins with the long repetitive amino acid tracts associated with these diseases recapitulates the protein aggregation that occurs in human disease. Here we show that the model organism Dictyostelium discoideum has evolved to normally encode long polyglutamine tracts and express these proteins in a soluble form. We also show that Dictyostelium has the capacity to suppress aggregation of a polyglutamine-expanded Huntingtin construct that aggregates in other model organisms tested. Together, these data identify Dictyostelium as a novel model organism with the capacity to suppress aggregation of proteins with long polyglutamine tracts.Entities:
Keywords: Dictyostelium; neurodegenerative disease; polyglutamine; protein aggregation; protein folding
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Year: 2015 PMID: 26330554 PMCID: PMC4646202 DOI: 10.1074/jbc.M115.676247
Source DB: PubMed Journal: J Biol Chem ISSN: 0021-9258 Impact factor: 5.157