| Literature DB >> 26256814 |
Yasuaki Tanaka1, Mihoko Kawabata1, Melvin M Scheinman2, Kenzo Hirao1.
Abstract
The QT interval in patients with catecholaminergic polymorphic ventricular tachycardia (CPVT) is typically normal. However, CPVT patients are sometimes misdiagnosed as concealed long QT syndrome (LQTS), because patients with LQTS also manifest with syncope or sudden death following periods of exertion or extreme emotion. We report a CPVT patient with a pathogenic RyR2 mutation associated with a marked QT prolongation, which normalized after flecainide therapy. ©2015 Wiley Periodicals, Inc.Entities:
Keywords: bidirectional ventricular tachycardia; catecholaminergic polymorphic ventricular tachycardia; flecainide; long QT syndrome; sudden cardiac death
Mesh：
Year: 2015 PMID： 26256814 DOI： 10.1111/pace.12735
Source DB: PubMed Journal: Pacing Clin Electrophysiol ISSN： 0147-8389 Impact factor: 1.976