Literature DB >> 26251926

Case study of remission in adults with immune thrombocytopenia following cessation of treatment with the thrombopoietin mimetic romiplostim.

James B Bussel1, Xuena Wang2, Angela Lopez2, Melissa Eisen2.   

Abstract

OBJECTIVES: In adults, immune thrombocytopenia (ITP), characterized by platelet counts <100 × 10(9)/l, is typically chronic, with remission reported infrequently ≥3 years post-diagnosis. The thrombopoietin mimetic romiplostim increases platelet counts and reduces use of concomitant ITP medications in chronic ITP. While often perceived as a long-term treatment, dose-adjustment rules allow romiplostim to be discontinued when hemostatic platelet counts are reached, as reported in Amgen trials.
METHODS: Eight romiplostim trials were examined for remission, defined as ≥26 consecutive weeks of platelets ≥50 × 10(9)/l without treatment.
RESULTS: Remission was identified in 27 patients; median (quartile 1 [Q1], quartile 3 [Q3]) ITP duration of 2.1 (0.5, 4.2) years, 17/27 (63%) having ITP for >1 year, mean baseline platelets 20.9 × 10(9)/l, median preremission maximum dose 3.0 µg/kg, 12/27 (44%) were splenectomized at baseline, and there were 40-276 cumulative weeks of romiplostim with median time to remission 7.1 months. DISCUSSION/
CONCLUSION: No clear-cut predictors of remission were apparent; however, a number of patients had ITP for <1 year and received romiplostim for <1 year.

Entities:  

Keywords:  Platelets; Remission; Thrombopoietin; Thrombopoietin receptor agonist

Mesh:

Substances:

Year:  2015        PMID: 26251926     DOI: 10.1179/1607845415Y.0000000041

Source DB:  PubMed          Journal:  Hematology        ISSN: 1024-5332            Impact factor:   2.269


  9 in total

1.  Elucidating the Mechanism of Action of the Attributed Immunomodulatory Role of Eltrombopag in Primary Immune Thrombocytopenia: An In Silico Approach.

Authors:  Maria L Lozano; Cristina Segú-Vergés; Mireia Coma; María T Álvarez-Roman; José R González-Porras; Laura Gutiérrez; David Valcárcel; Nora Butta
Journal:  Int J Mol Sci       Date:  2021-06-27       Impact factor: 5.923

Review 2.  Long-term safety and efficacy of romiplostim for treatment of immune thrombocytopenia.

Authors:  Prakash Vishnu; David M Aboulafia
Journal:  J Blood Med       Date:  2016-05-25

3.  Repeated successful use of eltrombopag in chronic primary immune thrombocytopenia: description of an intriguing case.

Authors:  Cristina Santoro; Paola Volpicelli; Erminia Baldacci; Grazia Ferrara; Alice Di Rocco; Antonietta Ferretti; Marika Porrazzo; Maria Gabriella Mazzucconi
Journal:  Clin Case Rep       Date:  2017-07-13

4.  Sustained Remission in Patients with Primary Immune Thrombocytopenia after Romiplostim Tapering and Discontinuation: A Case Series in Real Life Management in Spain.

Authors:  María-Eva Mingot-Castellano; Carlos Grande-García; David Valcárcel-Ferreiras; Clara Conill-Cortés; Loreto de Olivar-Oliver
Journal:  Case Rep Hematol       Date:  2017-06-11

Review 5.  Immunomodulation in Primary Immune Thrombocytopenia: A Possible Role of the Fc Fragment of Romiplostim?

Authors:  Alexandra Schifferli; Falk Nimmerjahn; Thomas Kühne
Journal:  Front Immunol       Date:  2019-06-04       Impact factor: 7.561

6.  Long-term treatment with romiplostim and treatment-free platelet responses in children with chronic immune thrombocytopenia.

Authors:  Michael D Tarantino; James B Bussel; Victor S Blanchette; Donald Beam; John Roy; Jenny Despotovic; Ashok Raj; Nancy Carpenter; Bhakti Mehta; Melissa Eisen
Journal:  Haematologica       Date:  2019-03-07       Impact factor: 9.941

7.  Tapering thrombopoietin receptor agonists in primary immune thrombocytopenia: Expert consensus based on the RAND/UCLA modified Delphi panel method.

Authors:  Adam Cuker; Jenny M Despotovic; Rachael F Grace; Caroline Kruse; Michele P Lambert; Howard A Liebman; Roger M Lyons; Keith R McCrae; Vinod Pullarkat; Jeffrey S Wasser; David Beenhouwer; Sarah N Gibbs; Irina Yermilov; Michael S Broder
Journal:  Res Pract Thromb Haemost       Date:  2020-12-08

8.  Second-line administration of thrombopoietin receptor agonists in immune thrombocytopenia: Italian Delphi-based consensus recommendations.

Authors:  Monica Carpenedo; Erminia Baldacci; Claudia Baratè; Alessandra Borchiellini; Francesco Buccisano; Giuseppina Calvaruso; Federico Chiurazzi; Bruno Fattizzo; Gaetano Giuffrida; Elena Rossi; Francesca Palandri; Potito Rosario Scalzulli; Sergio Mario Siragusa; Angelantonio Vitucci; Francesco Zaja
Journal:  Ther Adv Hematol       Date:  2021-10-09

Review 9.  A Review of Romiplostim Mechanism of Action and Clinical Applicability.

Authors:  James B Bussel; Gerald Soff; Adriana Balduzzi; Nichola Cooper; Tatiana Lawrence; John W Semple
Journal:  Drug Des Devel Ther       Date:  2021-05-26       Impact factor: 4.162

  9 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.