A Bariath Kelani1,2, H Moumouni3,4, H Younsa3,5, L James Didier3,5, A M Hima6, A Guemou6, A W Issa6, A Ibrahim6, M A Sanda6, R Sani3,5, S Sanoussi6,3, M Catala7,8,9,10. 1. Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger. akelani2@yahoo.fr. 2. Faculté des Sciences de la Santé, Service de Neurochirurgie, Hôpital National de Niamey (HNN), Université Abdou Moumouni (UAM), BP 12932, Niamey, Niger. akelani2@yahoo.fr. 3. Faculté des Sciences de la Santé, Service de Neurochirurgie, Hôpital National de Niamey (HNN), Université Abdou Moumouni (UAM), BP 12932, Niamey, Niger. 4. Département d'Histologie et Embryologie, UAM, Niamey, Niger. 5. Service de Chirurgie Générale, Hôpital National de Niamey, Niamey, Niger. 6. Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger. 7. Sorbonne Université, UPMC Université Paris 06, UMR7622, F-75005, Paris, France. 8. Institut de Biologie Paris Seine (IBPS) - Developmental Biology Laboratory, UMR7622, CNRS, F-75005, Paris, France. 9. INSERM, ERL1156, F-75005, Paris, France. 10. Fédération de Neurologie, Groupe hospitalier Pitié-Salpêtrière-APHP, F-75013, Paris, France.
Abstract
INTRODUCTION: Subcutaneous tumors with extra limbs are very rare, and they are considered either as fetus in fetu or fetiform teratoma. CASE REPORT: We report here the case of a 6-day-old presenting a mass extending at the level of the occipital bone. This mass is developed in the extracranial region and contains two forelimbs including hands with digits. CT shows that the squamous part of the occipital bone is involved with several defects through which a part of the cerebellum herniates. The boy was operated on and the tumor was removed. The herniated region of the cerebellum has also been removed. After surgery, the boy develops normally. CONCLUSION: This type of tumor is extremely rare and is only the second case that has been reported at this exact location. This could be the so-called céphalomélie described by Isidore Geoffroy Saint-Hilaire in a duck in his famous Treatise of Teratology (1836). The cause of this malformation is still a matter for debate.
INTRODUCTION:Subcutaneous tumors with extra limbs are very rare, and they are considered either as fetus in fetu or fetiform teratoma. CASE REPORT: We report here the case of a 6-day-old presenting a mass extending at the level of the occipital bone. This mass is developed in the extracranial region and contains two forelimbs including hands with digits. CT shows that the squamous part of the occipital bone is involved with several defects through which a part of the cerebellum herniates. The boy was operated on and the tumor was removed. The herniated region of the cerebellum has also been removed. After surgery, the boy develops normally. CONCLUSION: This type of tumor is extremely rare and is only the second case that has been reported at this exact location. This could be the so-called céphalomélie described by Isidore Geoffroy Saint-Hilaire in a duck in his famous Treatise of Teratology (1836). The cause of this malformation is still a matter for debate.
Authors: Ajay N Gangopadhyay; Arvind Srivastava; Punit Srivastava; Dinesh K Gupta; Shiv P Sharma; Vijayendra Kumar Journal: J Med Case Rep Date: 2010-03-25
Authors: A B Kelani; H Moumouni; A W Issa; H Younsaa; Hmu Fokou; R Sani; S Sanoussi; L J Denholm; J E Beever; M Catala Journal: Childs Nerv Syst Date: 2017-01-12 Impact factor: 1.475