Malignant paraganglioma (multiple, multicentric and metastatic) in a female patient with family history of paraganglioma.

Malignant paragangliomas are rare, but may occur especially in patients with familial forms of the disease. We present the case of a 23 year old woman diagnosed with bilateral carotid paraganglioma with distant and local metastases, associated to a family history of paraganglioma and we present a literature review.