Literature DB >> 26142172

Life-threatening acute pneumonitis in mixed connective tissue disease: a case report and literature review.

Eva Rath1, Shahin Zandieh2, Alexander Löckinger3, Mirko Hirschl4, Klaus Klaushofer1, Jochen Zwerina5.   

Abstract

Mixed connective tissue disease (MCTD) is a rare connective tissue disease frequently involving the lungs. The main characteristic is a systemic sclerosis-like picture of slowly progressing interstitial lung disease consistent with lung fibrosis, while pulmonary arterial hypertension is rare. Herein, we present a case of a newly diagnosed MCTD patient developing life-threatening acute pneumonitis similar to lupus pneumonitis. Previous literature on this exceptionally rare complication of MCTD is reviewed and differential diagnosis and management discussed.

Entities:  

Keywords:  Acute respiratory failure; Mixed connective tissue disease; Pneumonitis

Mesh:

Year:  2015        PMID: 26142172     DOI: 10.1007/s00508-015-0823-6

Source DB:  PubMed          Journal:  Wien Klin Wochenschr        ISSN: 0043-5325            Impact factor:   1.704


  7 in total

1.  Mixed connective tissue disease presenting with pneumonitis and pneumatosis intestinalis.

Authors:  C Fernandes; P Bungay; B R O'Driscoll; A L Herrick
Journal:  Arthritis Rheum       Date:  2000-03

Review 2.  Prevalence of pulmonary hypertension in an unselected, mixed connective tissue disease cohort: results of a nationwide, Norwegian cross-sectional multicentre study and review of current literature.

Authors:  Ragnar Gunnarsson; Arne K Andreassen; Øyvind Molberg; Åse Stavland Lexberg; Kari Time; Alvilde Sofie Strand Dhainaut; Liv-Turid Bertelsen; Øyvind Palm; Karen Irgens; Andrea Becker-Merok; Jan Leidulf Nordeide; Villy Johnsen; Sonja Pedersen; Anne Prøven; Lamya Samir Noori Garabet; Torhild Garen; Trond Mogens Aaløkken; Inge-Margrethe Gilboe; Jan Tore Gran
Journal:  Rheumatology (Oxford)       Date:  2013-02-12       Impact factor: 7.580

3.  Prevalence and severity of interstitial lung disease in mixed connective tissue disease: a nationwide, cross-sectional study.

Authors:  Ragnar Gunnarsson; Trond Mogens Aaløkken; Øyvind Molberg; May Brit Lund; Georg Karl Mynarek; Ase Stavland Lexberg; Kari Time; Alvilde Sofie Strand Dhainaut; Liv-Turid Bertelsen; Oyvind Palm; Karen Irgens; Andrea Becker-Merok; Jan Leidulf Nordeide; Villy Johnsen; Sonja Pedersen; Anne Prøven; Lamya Samir Noori Garabet; Jan Tore Gran
Journal:  Ann Rheum Dis       Date:  2012-05-01       Impact factor: 19.103

Review 4.  Respiratory manifestations of systemic lupus erythematosus: old and new concepts.

Authors:  José María Pego-Reigosa; Dina A Medeiros; David A Isenberg
Journal:  Best Pract Res Clin Rheumatol       Date:  2009-08       Impact factor: 4.098

5.  Rapidly progressive respiratory failure in mixed connective tissue disease: report of an autopsy case.

Authors:  Yasutaka Watanabe; Shinichiro Koyama; Masato Moriguchi; Chihiro Miwa; Mamoru Shiraishi; Motoko Nomura; Mitsuhiro Nokubi; Chihiro Terai; Yoshinori Kawabata
Journal:  Intern Med       Date:  2012-12-15       Impact factor: 1.271

Review 6.  The diagnosis and classification of mixed connective tissue disease.

Authors:  Chiara Tani; Linda Carli; Sabrina Vagnani; Rosaria Talarico; Chiara Baldini; Marta Mosca; Stefano Bombardieri
Journal:  J Autoimmun       Date:  2014-01-22       Impact factor: 7.094

7.  [A case of mixed connective tissue disease with acute interstitial pneumonitis].

Authors:  T Takeda; A Tsutsumi; N Ogura; S Jodo; Y Amasaki; T Nakabayashi; A Fujisaku; S Kobayashi; T Koike
Journal:  Nihon Rinsho Meneki Gakkai Kaishi       Date:  1995-06
  7 in total

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