| Literature DB >> 26142172 |
Eva Rath1, Shahin Zandieh2, Alexander Löckinger3, Mirko Hirschl4, Klaus Klaushofer1, Jochen Zwerina5.
Abstract
Mixed connective tissue disease (MCTD) is a rare connective tissue disease frequently involving the lungs. The main characteristic is a systemic sclerosis-like picture of slowly progressing interstitial lung disease consistent with lung fibrosis, while pulmonary arterial hypertension is rare. Herein, we present a case of a newly diagnosed MCTD patient developing life-threatening acute pneumonitis similar to lupus pneumonitis. Previous literature on this exceptionally rare complication of MCTD is reviewed and differential diagnosis and management discussed.Entities:
Keywords: Acute respiratory failure; Mixed connective tissue disease; Pneumonitis
Mesh:
Year: 2015 PMID: 26142172 DOI: 10.1007/s00508-015-0823-6
Source DB: PubMed Journal: Wien Klin Wochenschr ISSN: 0043-5325 Impact factor: 1.704