Literature DB >> 2613240

Analysis of molecular deletions with cDNA probes in patients with Duchenne and Becker muscular dystrophies.

H Gilgenkrantz1, J Chelly, M Lambert, D Récan, J C Barbot, G J van Ommen, J C Kaplan.   

Abstract

In the course of a systematic survey of DMD and BMD patients with intronic probes and with cDNA probes covering three-fourths of the coding sequence, 45 molecular deletions within the DMD gene were investigated. Forty-two percent of the breakpoints were located in the intronic sequence containing probe P20, whereas the other deletions were widespread around the more proximal part of the gene. Most of the BMD deletions were in the P20 region. Pulsed field gel electrophoresis was used to determine the size of some deletions and allowed us to estimate the physical distance between the intronic probes JBir and P20. The reading frame was checked in 11 cases with proximal deletions and found to be disrupted in 6 of 7 DMD patients, in 1 intermediate case, and, unexpectedly, in 3 BMD patients.

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Year:  1989        PMID: 2613240     DOI: 10.1016/0888-7543(89)90025-6

Source DB:  PubMed          Journal:  Genomics        ISSN: 0888-7543            Impact factor:   5.736


  8 in total

1.  Duplicational mutation at the Duchenne muscular dystrophy locus: its frequency, distribution, origin, and phenotypegenotype correlation.

Authors:  X Y Hu; P N Ray; E G Murphy; M W Thompson; R G Worton
Journal:  Am J Hum Genet       Date:  1990-04       Impact factor: 11.025

2.  Molecular deletion patterns in families from southern France with Duchenne/Becker muscular dystrophies.

Authors:  M Claustres; S Tuffery; M P Chevron; M P Jozelon; P Martinez; B Echenne; J Demaille
Journal:  Hum Genet       Date:  1991-12       Impact factor: 4.132

3.  Patterns of deletions of the dystrophin gene in different European populations.

Authors:  G A Danieli; F Mioni; C R Müller; L Vitiello; M L Mostacciuolo; T Grimm
Journal:  Hum Genet       Date:  1993-05       Impact factor: 4.132

4.  The clinical, genetic and dystrophin characteristics of Becker muscular dystrophy. II. Correlation of phenotype with genetic and protein abnormalities.

Authors:  K M Bushby; D Gardner-Medwin; L V Nicholson; M A Johnson; I D Haggerty; N J Cleghorn; J B Harris; S S Bhattacharya
Journal:  J Neurol       Date:  1993-02       Impact factor: 4.849

5.  Genotype-phenotype correlation and germline mosaicism in DMD/BMD patients with deletions of the dystrophin gene.

Authors:  A E Covone; M Lerone; G Romeo
Journal:  Hum Genet       Date:  1991-07       Impact factor: 4.132

6.  Illegitimate transcription. Application to the analysis of truncated transcripts of the dystrophin gene in nonmuscle cultured cells from Duchenne and Becker patients.

Authors:  J Chelly; H Gilgenkrantz; J P Hugnot; G Hamard; M Lambert; D Récan; S Akli; M Cometto; A Kahn; J C Kaplan
Journal:  J Clin Invest       Date:  1991-10       Impact factor: 14.808

7.  Dystrophin analysis using a panel of anti-dystrophin antibodies in Duchenne and Becker muscular dystrophy.

Authors:  F Muntoni; A Mateddu; C Cianchetti; M G Marrosu; A Clerk; M Cau; R Congiu; A Cao; M A Melis
Journal:  J Neurol Neurosurg Psychiatry       Date:  1993-01       Impact factor: 10.154

8.  Screening for mutations in the muscle promoter region and for exonic deletions in a series of 115 DMD and BMD patients.

Authors:  L Vitiello; M L Mostacciuolo; S Oliviero; F Schiavon; L Nicoletti; C Angelini; G A Danieli
Journal:  J Med Genet       Date:  1992-02       Impact factor: 6.318

  8 in total

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